Giant hydronephrotic kidney in adolescence- A rare case report and a review of the literature

Abstract

Giant hydronephrotic kidney is a rare form of obstructive uropathy in adolescents. We report a 19 year old girl with huge abdominal distention secondary to hydronephrotic kidney. The cystic swelling occupied whole of the abdominal cavity with other structures being compressed. She presented with progressive distention of abdomen with early satiety. Subsequently ultrasonological and CT scan evaluation revealed a giant hydronephrosis of right kidney occupying almost whole abdomen. Such presentation of PUJ obstruction is rare. We present this case in which percutaneous nephrostomy with slow decompression was done as initial treatment to relieve symptoms and prevent complications.

Giant hydronephrosis secondary to ureteropelvic junction obstruction, a rare occurrence, case report

“…UPJ obstruction is the commonest cause of giant hydronephrosis, other causes include urinary stones, trauma, renal ectopia, ureterovesical junction obstruction, and rarely malignancies. 4 …”

Acute Presentation of Giant Hydronephrosis in an Adult

“…Giant hydronephrosis is the presence of more than one liter of fluid in the collecting system of a hydronephrotic kidney. Although it is classically caused by UPJO, other conditions such as ovarian cysts, pancreatic cysts, hydatid cysts, and large adrenal cysts can mimic this peculiar condition of the kidney [ 4 ]. With the advent of imaging facilities and widespread abdominal imaging, hydronephrosis is picked up early in the course, and giant hydronephrosis is rarely diagnosed.…”

Giant hydronephrosis management in the Era of minimally invasive surgery: A case series

“…The first case of GH was described in 1746. Since then, few cases have been described in the literature [ 1 ]. This condition is a rare urological entity, defined in the literature as more than 1 L of fluid or fluid amounting to at least 1.6% of one’s body weight, contained in the collecting system.…”

“…Giant hydronephrosis (GH) is a rare urological entity, described in the literature as more than 1 L of fluid contained in the renal collecting system [ 1 ]. Its presentation is usually vague, but it is most frequently associated with abdominal distention.…”

“…Its presentation is usually vague, but it is most frequently associated with abdominal distention. The most common cause of the condition, described in the literature, is ureteropelvic junction obstruction (UPJO) [ 1 ]. A limited number of cases of adult GH has been reported.…”