<p class="abstract">Its a case report of, Goldenhar syndrome (GS), a rare syndrome with right ear microtia, atresia of the external auditory canal, nasal polyposis, pulmonary agenesis, spine abnormalities and dextrocardia. This case, has showed the involvement of nose in the form of nasal polyposis in GS, which has never been reported in the literature so far.</p>