Hemangioblastoma quístico de la unión bulbomedular asociado a enfermedad de von Hippel-Lindau. Presentación de dos casos y revisión de la bibliografía

Cystic hemangioblastoma of the brainstem

“…[11] With the incorporation of the latest neuroimaging and microsurgery techniques, complete and safe microsurgical resection of brain stem hemangioblastomas, without any kind of postoperative neurological deficits is feasible. [1,2,4,10,11] However, postoperative care is mandatory to reduce the operative mortality and morbidity (due to the likelihood of respiratory and circulatory disorders, and bulbar palsy). [10,[12][13][14] The solid nodule tumor mass is removed microscopically by dissecting the gliotic margins away from the tiny vascular pedicles that are coagulated, however the removal of the cyst wall is not necessary.…”

“…Hemangioblastomas are very highly vascular neoplasm with benign characteristics representing between 2-3% of brain tumors and; only 5-20% of hemangioblastomas are located in the brainstem. [1][2][3][4] The junction of the medulla and upper spinal cord is a less common site where these lesions are diagnosed. [1,3,4] In comparison to cerebellar haemangioblastoma, cystic hemangioblastoma of the brain stem is rare with only a few case reports in literature (the size of mural nodules varies between 6 and 20 mm in diameter).…”

“…[1][2][3][4] The junction of the medulla and upper spinal cord is a less common site where these lesions are diagnosed. [1,3,4] In comparison to cerebellar haemangioblastoma, cystic hemangioblastoma of the brain stem is rare with only a few case reports in literature (the size of mural nodules varies between 6 and 20 mm in diameter). [1,3,[5][6][7][8]…”

“…[1,3,4] In comparison to cerebellar haemangioblastoma, cystic hemangioblastoma of the brain stem is rare with only a few case reports in literature (the size of mural nodules varies between 6 and 20 mm in diameter). [1,3,[5][6][7][8]…”