Hemidystonia and Hemichoreoathetosis as an Initial Manifestation of Moyamoya Disease

Abstract

To our knowledge, this is the first report of an adult patient presenting with hemidystonia and hemichoreoathetosis as the initial manifestations of moyamoya disease. Arch Neurol. 2000;57:1510-1512

Hyperventilation-Enhanced Chorea as a Transient Ischaemic Phenomenon in a Patient with Moyamoya Disease

“…Chorea is a comparatively rare clinical feature of moyamoya disease and moyamoya syndrome, which in few cases seems to be the initial manifestation leading to the diagnosis [5,15,16,19,20]. This case demonstrates the need to include this uncommon pathological entity in the differential diagnosis of juvenile or adult onset chorea.…”

“…Epileptic seizures, migrainous headaches, transient ischaemic attacks or ischaemic strokes in children and haemorrhagic strokes in adults are the cardinal initial manifestations of this uncommon cerebrovascular disease [1][2][3][4]. Involuntary movements, such as dyskinesia, chorea or hemiballismus [1,5], behavioural disturbances [6], neuropsychological deficits and mental deterioration [7] have rarely been described. Moyamoya disease has to be distinguished from the secondary moyamoya syndrome, which occurs mostly unilaterally and is associated with a series of other diseases [1,8,9].…”

Reversible striatal hypermetabolism in chorea associated with moyamoya disease: a report of two cases

“…Elimination of the chorea was confirmed when she visited our clinic 2 months after onset. 18 F-FDG PET performed at that time revealed normalized glucose metabolism in the right striatum (Fig. 2).…”

“…Magnetic resonance imaging (MRI) revealed a small asymptomatic ischemic lesion in the right frontal white matter. 18 F-FDG PET revealed markedly elevated glucose metabolism in the right striatum (Fig. 2).…”

Involuntary Movements Induced and Remitted by Indirect Bypass Surgery in a Patient with Moyamoya Disease

“…Table 1 summarizes clinical characteristics of 13 patients with moyamoya disease with involuntary movement including the present case [6][7][8][9][10][11][12][13][14][15][16]. There were 2 men (15.4%) and 11 women (84.6%) identified with a mean age of 21.3 years ranging from 7 to 54.…”