The Congenital heart diseases are characterized by morphological defects in the embryonic development and the most frequent in dogs are: pulmonary and aortic valve stenosis, ventricular septal defect and persistent ductus arteriosus. They may occur asymptomatically or even evolve to congestive heart failure. The definitive diagnosis is made through the visualization of the alterations in the echocardiogram. In the present report, a French Bulldog, three months old, asymptomatic was presented to a private Veterinary practice in Rio de Janeiro, Brazil. Cardiac auscultation evidenced a systolic heart murmur in tricuspid focus and diastolic murmur in pulmonary focus. To better evaluate the dog chest radiography, electrocardiogram and echocardiogram were performed and allowed the diagnosis of pulmonary stenosis. The clinical treatment with beta-blocker was installed and the surgical procedure was performed with the balloon valvuloplasty. After the surgical treatment, the pressure gradient was gradually normalized, the use of atenolol was discontinued, and the patient was followed up for three years, remaining clinically stable throughout this time. The aim of this study was to report a case of pulmonary artery stenosis in a puppy, treated clinically and surgically, emphasizing the importance of the physical and complementary cardiological exams.