High-resolution computed tomography in detection of lung pathology in patients with connective tissue dysplasia

Abstract

SummaryThis article presents results of examination of 50 young patients with connective tissue dysplasia not having any acute or chronic respiratory disease. All patients underwent inspiratory and expiratory helical CT with density gradient determination in different parts of the lungs. Typical CT findings were subpleural apical bullae and bleby (16 %), peribronchial fibrosis (40 %), local fibrosis (18 %), plevroapikal spikes (62 %), emphysema (4 %), air traps (18 %). The density gradient between exhalation and inhalation was reduced in the upper and lower lobes of the lungs.