Histiocytosis X of the temporal bone

Langerhans’ cell histiocytosis of the temporal bone in children

“…The incidence of LCH is around 5.4 per million and it is a rare entity with a male predominance (male to female ratio of 1.7:1) [2,9]. Temporal bone involvements in LCH and otoneurological symptoms are seen in 4-25% of cases [4]. In our study, 17% of LCH cases were associated with temporal bone involvement with a male to female ratio of 1.5:1.…”

“…It is a rare entity with a male predominance [2]. Its peak incidence period is noted in children aged between 1 and 4 years, but it can affect patients of any age [1,4].…”

“…It can range from a multifocal to a solitary lesion. It usually affects the head and neck, mainly the skull base, in 60% of cases [3,4]. The temporal bone is involved in 19-25% of cases and the involvement is bilateral in a third of all cases [2,5].…”

Langerhans cell histiocytosis of the temporal bone in a child

“…It mainly affects children of age between 1 to 4 years. [1,4] The clinical presentation of LCH depends upon the site of involvement. It can range from a multifocal to a solitary lesion.…”

“…It usually affects the head and neck, mainly the skull base, in 60% of cases. [3,4] The temporal bone is involved in 19-25% of cases and the involvement is bilateral in a third of all cases. [2,5] The petrous ridge of the temporal bone is the most commonly affected area.…”