Hypoplastic left heart with absence of the aortic valve: Prenatal diagnosis using two‐dimensional and pulsed Doppler echocardiography

Cartier, M S; Emerson, Donald E.; Plappert, Theodore; Sutton, Martin St. John

doi:10.1002/jcu.1870150707

Cited by 7 publications

(3 citation statements)

References 9 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Interestingly, case 5 showed internal echogenic lining or bright endocardium of the small LV, probably representing endocaridial fibroelastosis, which has been associated with HLHS. 4,5 Hypoplastic ascending aorta was observed in all of the cases presented here. The size of the aorta and where it arises will also determine the prognosis postnatally, so a complete evaluation of this defect always includes determination of the size of the aorta from the aortic valve to the ductus arteriosus.…”

Section: Discussionmentioning

confidence: 71%

See 1 more Smart Citation

Prenatal sonographic features of isolated hypoplastic left heart syndrome

Tongsong

Sittiwangkul

Khunamornpong

et al. 2005

J. Clin. Ultrasound

View full text Add to dashboard Cite

Hypoplastic left heart syndrome (HLHS) is a spectrum of fetal conditions associated with severe hypoplasia of the left ventricle and left ventricular outflow tract. The purpose of this series was to focus on the sonographic prenatal features of isolated HLHS. Based on the 5 cases presented here, the prenatal sonographic features of HLHS include small-sized left ventricle, atretic or hypoplastic mitral valves with restricted motion and a small amount of antegrade flow or regurgitation, and hypoplastic ascending aorta. Retrograde flow in the transverse aortic arch strongly suggests inadequate systemic output from the left heart. Tricuspid regurgitation is common and increases the chance for the development of hydrops. Other findings may be helpful, including left ventricular hyperechoic endocardium and increased nuchal translucency at 11-14 weeks. With careful fetal echocardiography, HLHS may be readily observed on a 4-chamber view as either a small or even absent left ventricle.

show abstract

Section: Discussionmentioning

confidence: 71%

“…Although HLHS is the leading cause of cardiac death in the neonatal period and several prenatal series have been reported few reports have focused on prenatal sonographic features of HLHS. 4,5 The objective of this small series was to describe the sonographic prenatal features of isolated HLHS without extracardiac abnormalities.…”

mentioning

confidence: 99%

Prenatal sonographic features of isolated hypoplastic left heart syndrome

Tongsong

Sittiwangkul

Khunamornpong

et al. 2005

J. Clin. Ultrasound

View full text Add to dashboard Cite

show abstract

“…For instance, in hypoplastic left heart syndrome, a hypo· plasia left ventricle, hypoplastic of the mitral valve, aortic valvular atresia, and aortic arch anomalies are seen. 20 The sonographic spectrum of abnormalities of the hypoplastic left heart are well illustrated in Figures 1 and 2. In Figure 1 the fetus essentially has a twochambered heart with either a single atrium or two atria with a large atrial septal defect and a single ventricle.…”

Section: Ultrasound Examinationmentioning

confidence: 96%

Sonographic spectrum of fetal cardiac hypoplasia.

McGahan

Choy²,

Parrish³

et al. 1991

Journal of Ultrasound in Medicine

View full text Add to dashboard Cite

Four cases of hypoplastic left ventricle and three cases of hypoplastic right ventricle detected sonographically prenatally are presented. A four-chamber view of the heart was abnormal in all seven cases. The sonographic appearance of the hypoplastic ventricle was variable, being smaller than normal in six of seven cases and not being identified at all in one case. Other ultrasound findings included an atrial septal defect (11 = 7); increased size of the contralateral ventricle (n = 6); nonvisualization or poor visualization of the outflow tract of the affected ventricle (11 -6), and intact ventricular septum (11 == S). In one of four cases of hypoplastic left ventricle the pregnancy was terminated; the other three infants died within 5 days after birth. One H eart disease is the most common severe congenital anomaly found in live births and is a major cause of death from congenital anomalies in childhood.1 It has been estimated that structural abnormalities of the heart and the great vessels are among the most common fetal malformations, occur~ ring more frequently than in 8 of 1,000 live births.' Unfortunately, a number of cardiac malformations produce serious morbidity and high mortality rates within the first month of life but may not be recognized prenatally. For example, hypoplastic left heart syn· drome usually results in death within 4 weeks after birth. Right ventricular outflow tract abnormalities, such as pulmonary atresia with an intact septum re-

show abstract

References

2003

The Natural and Modifed History of Congenital Heart Disease

View full text Add to dashboard Cite

Hypoplastic left heart with absence of the aortic valve: Prenatal diagnosis using two‐dimensional and pulsed Doppler echocardiography

Cited by 7 publications

References 9 publications

Prenatal sonographic features of isolated hypoplastic left heart syndrome

Prenatal sonographic features of isolated hypoplastic left heart syndrome

Sonographic spectrum of fetal cardiac hypoplasia.

References

Contact Info

Product

Resources

About