Identification and management of fetal isolated right‐sided aortic arch in an unselected population

Abstract

RAA can be identified easily on a routine fetal anomaly scan, however the prevalence of RAA is low in an unselected population. Antenatally diagnosed cases should be referred for detailed fetal echocardiography and the patient should be made aware of the association with DiGeorge syndrome and the symptoms associated with a vascular ring. Copyright © 2016 ISUOG. Published by John Wiley & Sons Ltd.

Fetal right aortic arch: associated anomalies, genetic anomalies with chromosomal microarray analysis, and postnatal outcome

“…As published reports described, fetal RAA with a left ductus was a predominant finding in our series (73.2% of cases). If the cases with intracaridac anomalies were excluded, the prevalence rate of left ductus was about 95%, which was similar to previous stuides . Fetal RAA with a left ductus is more obvious, presenting a U‐sign on 3VT view, unfortunately RAA with a right ductus is more insidious.…”

Right aortic arch with situs solitus frequently heralds a vascular ring

“…Some consider that a RAA is often a normal anatomical variant; however, apart from situs inversus with dextrocardia in which a RAA is expected, an isolated RAA with situs solitus and a mirror image arterial branching pattern is exceedingly uncommon . We encountered only one such patient in our cohort.…”

Prenatal diagnosis and clinical implications of an apparently isolated right aortic arch

“…In relation to prenatal management, there is contradictory evidence concerning the association with chromosomal and genetic abnormalities and therefore the option for invasive diagnostic testing. For example, in relation to the association with 22q11 microdeletion in some studies, the incidence was as high as 15% and in others as low as 0% . In relation to postnatal management, there is no clear evidence‐based pathway despite the fact that a RAA with a left arterial duct represents an anatomical vascular ring that encircles the trachea and esophagus.…”