Interrupted aortic arch with multiple vascular malformations

Xiang, Xiaorui; Chen, Zixian; Zhang, Li; Lei, Junqiang; Guo, Shunlin

doi:10.1097/cm9.0000000000000438

Cited by 4 publications

(3 citation statements)

References 4 publications

(4 reference statements)

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“…In contrast, no obvious anatomical interruption was detected in CoA case with the narrowing between the above-mentioned arteries. According to previous reports, although the definitions of type A IAA and CoA were different, the clinical manifestations were similar in increased blood pressure, which was higher in the upper limbs than in the lower limbs[ 7 - 12 ]. The manifestations of Cases 1 and 2 in this study were consistent with these reports.…”

Section: Discussionmentioning

confidence: 99%

Difference and similarity between type A interrupted aortic arch and aortic coarctation in adults: Two case reports

Ren¹,

Zhang²,

Li³

et al. 2022

WJCC

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BACKGROUND Aortic coarctation (CoA) is usually confused with interrupted aortic arch (IAA), especially adult type A interrupted aortic arch, due to their similar anatomical location. Although the main difference between them is whether arterial lumen exhibits continuity or not, the clinical manifestations are similar and connection exists between them. Adult type A IAA is considered as an extreme form of CoA, which is complete discontinuity of aortic function and lumen caused by degenerative arterial coarctation. This paper reports two cases (interrupted aortic arch and severe aortic coarctation) to analyze the difference and similarity between them. CASE SUMMARY The two cases of patients presented with hypertension for many years. Computed tomography angiography showed that the aortic arch and descending aorta were discontinuous or significantly narrowed with extensive collateral flow. The IAA patient refused surgical treatment and blood pressure could be controlled with drugs. While the CoA patient underwent stent implantation because of uncontrollable hypertension, the blood flow recovered smoothly and the blood pressures at both ends of the stenosis returned to normal after surgery. CONCLUSION Adult type A IAA and CoA have difference and similarity, and type A IAA is associated with CoA to a certain extent. The treatment method should be chosen based on the patient's clinical symptoms rather than the severity of the lesion.

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Section: Discussionmentioning

confidence: 99%

Difference and similarity between type A interrupted aortic arch and aortic coarctation in adults: Two case reports

Ren¹,

Zhang²,

Li³

et al. 2022

WJCC

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“…Imaging studies such as echocardiography, magnetic resonance imaging (MRI), computed tomography angiography (CTA), and recently dual-source computed tomography (DSCT) are being widely used as evaluation studies [8]. CTA is the gold standard for evaluating aortic interruption [9]. Early diagnosis of congenital heart defects including evaluation of the aorta and coronaries is important for better management strategies [10,11].…”

Section: Discussionmentioning

confidence: 99%

Unraveling the Trio of Interrupted Descending Aorta, Aortic Stenosis, and Bicuspid Aortic Valve: A Complex Cardiovascular Conundrum

Toshniwal,

Agrawal,

Chaturvedi

et al. 2023

Cureus

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Interrupted descending aorta (IDA) is an extremely rare congenital heart defect characterized by a complete loss of connection between the ascending and descending aorta. This condition is typically diagnosed in infancy or early childhood, but there have been very few cases reported in adulthood. Here, we present a unique case of an IDA in a 16-year-old patient with concomitant aortic stenosis (AS) and bicuspid aortic valve (BAV), making it an extremely rare scenario. This case highlights the importance of early diagnosis and appropriate management in patients with an IDA, particularly when in association with other cardiovascular abnormalities.

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“…Depending on the location of the interruption of the arch, IAA is classified into 3 types 5,8 . Type A IAA is characterized by an interruption located after the origin of the left subclavian artery, it is the second most common type of IAA and it is found in 30% to 40% of cases and it is associated mainly to hemodynamic factors related to blood flow 5. Type B IAA occurs due to an interruption between the site of origin of the common carotid and left subclavian arteries, it is the most common type of IAA, comprising 50% to 60% of cases and it is more closely related with DiGeorge Syndrome 5,7 .…”

Section: Introductionmentioning

confidence: 99%

Clinical and Post-Surgical Features and Outcomes in Post-Surgical Patients with Aortic arch Interruption at a Specialty Hospital in Bogotá Between 2006 and 2019. Retrospective Multivariable Analysis

Rios Dueñas

2022

IJCCI

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Introduction. Interruption of the aortic arch due to absence of tissue between the ascending and descending portions of the aorta is a pathology of low incidence, yet it has a mortality rate of nearly 90% within the first year of life. Surgical intervention is aimed at re-establishing continuity of the vessel, as well as correcting associated lesions through closure of IVC or performing a pulmonary artery cerclage correction. The mortality is 18% to 42%. The survival rate is close to 73% at one month, 65% at one year and 63% at 3 years after surgery. Materials and Methods. Review of Cardiovascular Surgery database between 2006 and 2019, identifying patients who underwent surgery due to aortic arch interruption. Results. In the last 4 years, an institutional technique was introduced, using pericardium tissue for reconstruction and partial junction of the descending aorta with the arch through advancement of the arterial cannulae towards the brachiocephalic trunk and has been positively associated to brain protection. Since, results have improved: lower tissue traction, greater amplitude of the neoarch and better neurological outcomes have been achieved. The objective of this paper is to identify the most important factors that ultimately determine prognosis and survival of patients with these pathologies, as well as to describe results of the implemented technique. Discussion. Aortic arch surgery is considered to be highly complex. Results yielded in this research showed a high mortality within the first years, which decreased into a similar rate to that of medical literature. The main factors associated with complications identified were a late diagnosis and malnutrition. In addition, morbidity and mortality rates were similar to those reported worldwide.

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Interrupted aortic arch with multiple vascular malformations

Cited by 4 publications

References 4 publications

Difference and similarity between type A interrupted aortic arch and aortic coarctation in adults: Two case reports

Difference and similarity between type A interrupted aortic arch and aortic coarctation in adults: Two case reports

Unraveling the Trio of Interrupted Descending Aorta, Aortic Stenosis, and Bicuspid Aortic Valve: A Complex Cardiovascular Conundrum

Clinical and Post-Surgical Features and Outcomes in Post-Surgical Patients with Aortic arch Interruption at a Specialty Hospital in Bogotá Between 2006 and 2019. Retrospective Multivariable Analysis

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