Isolated Supravalvular Stenosing Ring of Left Atrium: Diagnosis Before Operation and Successful Surgical Treatment

“…Its morphology ranges from a thin membrane to thick discrete fibrous ridge partially or completely encircling the mitral orifice leaflets [1]. Occasionally isolated [2], mitral ring is more often associated with other left-sided obstructive lesions [3]. CMS presents with degrees of severity that vary from an obstruction of little significance involving a structurally normal mitral valve to severe mitral stenosis.…”

Section: Discussionmentioning

confidence: 99%

The added value of real-time three-dimensional echocardiography in the diagnosis of supravalvar mitral ring: case report and review of the literature

et al. 2011

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Supravalvular mitral stenosis is a rare condition characterized by an abnormal ridge, with one or two orifices, covering and obstructing the mitral valve. Preoperative identification of the supravalvular ring is the target for obtaining good surgical results. Two-dimensional echocardiogram and transesophageal echocardiography both failed in reaching this objective. In this case, we showed that three-dimensional echocardiogram is a new technique that provides additional and more accurate echocardiographic characterization of congenital supravalvular mitral stenosis.

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“…Pre-operative identification of the membrane is possible by TEE [11,12], where angiography often fails [13]. However, there are still many limitations in visualization of the membrane, that is usually very thin; in this case, we performed an MRI examination, but as described in other papers [14,15], there was a failure in the detection of the supravalvular mitral ring.…”

Section: Discussionmentioning

confidence: 99%

Mitral supravalvular ring: a case report

Serra¹,

Testa²,

Ardissino³

2005

Cardiovasc Ultrasound

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Supravalvular mitral stenosis is a rare condition characterized by an abnormal ridge, with one or two orifices, covering and obstructing the mitral valve. Preoperative diagnosis is difficult with transtoracic echo (TTE), angiography and magnetic resonance imaging (MRI).In this case, a 36-year-old male, was admitted to our Heart department: He experienced progressive dyspnea on effort and at rest.Diagnosis was made by transesophageal echocardiography which showed, on apical 4-chamber section, an anulare structure attached since a membrane to the atrial wall anterior mitral valve leaflet and just proximal to the posterior mitral leaflet.Pre-operative identification of the supravalvular mitral ring is the target for obtaining good surgical results. Cineangiography and MRI both failed in reaching this objective, whereas, transesophageal echocardiography is the best method to identify this congenital heart disease.Using TEE the identification is not only possible but also easier.

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Isolated Supravalvular Stenosing Ring of Left Atrium: Diagnosis Before Operation and Successful Surgical Treatment

Cited by 33 publications

References 15 publications

Surgical strategies and outcomes in patients with supra-annular mitral ring: a single-institution experience☆

Surgical strategies and outcomes in patients with supra-annular mitral ring: a single-institution experience☆

The added value of real-time three-dimensional echocardiography in the diagnosis of supravalvar mitral ring: case report and review of the literature

Mitral supravalvular ring: a case report

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