Lack of connection between the atria and the peripheral conduction system in a case of corrected transposition with congenital atrioventricular block

Fetal Bradycardia Associated With Congenital Heart Defects – Is There a Clinicohistological Correlation? –

“…6, 7 Histologic investigation has disclosed that fibrosis and disruption in an elongated non-branching His bundle, together with fibrosis, occurs at the junction with the anterior node in situs solitus with L-loop CCTGA (without pulmonary atresia). [8][9][10] Electrophysiologic observations are consistent with the histological studies of CCTGA. 11…”

ACC/AHA 2008 Guidelines for the Management of Adults With Congenital Heart Disease

“…Conduction abnormalities are also common, with spontaneous complete heart block occurring at a rate of approximately 2% per year, and they are related to the abnormal position of the AV node (180,591,592). Complete AV block is common after surgical repair of a VSD or SAVV replacement, because the His bundle usually passes along the rim of the VSD.…”

ACC/AHA 2008 Guidelines for the Management of Adults With Congenital Heart Disease

“…180 Conduction abnormalities are also common, with spontaneous complete heart block occurring at a rate of approximately 2% per year, and they are related to the abnormal position of the AV node. 180,591,592 Complete AV block is common after surgical repair of a VSD or SAVV replacement, because the His bundle usually passes along the rim of the VSD.…”