Lebercirrhose bei Morbus Osler, Cirrhosis hepatis teleangiectatica

Ga, Martini

doi:10.1159/000200137

Cited by 20 publications

(4 citation statements)

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“…fully explained. In this case a history of nose bleeds affecting the patient and two members of his family suggested hereditary haemorrhagic telangiectasia, which may be associated with liver disease (Martini, 1955), but no evidence of cutaneous or mucosal telangiectasia was found on examination of the patient and his family.…”

Section: Investigationsmentioning

confidence: 65%

Cyanosis with hepatic cirrhosis: A case with pulmonary arteriovenous shunting

Karlish

Marshall²,

Reid

et al. 1967

Thorax

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A case is reported of cirrhosis of the liver associated with cyanosis and finger clubbing in a man of 31 years. The chest radiograph showed diffuse nodular shadows in both lower zones. Pulmonary function tests gave an arterial oxygen saturation of 91 % at rest, falling to 68% on exercise; the single breath diffusing capacity for carbon monoxide was reduced to 55% of the predicted value and there was an estimated right-to-left shunt of 23%. Post-mortem injection of the lungs with Micropaque-gelatin suspension showed numerous pleural spider naevi, denser over the lower lobes, arteriovenous communications in the infrahilar regions, including leashes of dilated vessels in pleural adhesions on the diaphragm and diffuse arterial vasodilatation in the lungs; although the injection mass could be traced into the pulmonary veins in only a few regions of the lung, the dilated arterioles and spiders were possible additional channels through which blood might be shunted from the alveolar surfaces. The very low arterial oxygen saturation on exercise was probably caused by a shunt greater than the 23 % estimated at rest, but the low diffusing capacity may have been partly responsible. The cause of the low diffusing capacity remains uncertain.

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Section: Investigationsmentioning

confidence: 65%

Cyanosis with hepatic cirrhosis: A case with pulmonary arteriovenous shunting

Karlish

Marshall²,

Reid

et al. 1967

Thorax

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“…Angiography was not yet available. Five additional cases were added by the author including two a description of which had been previously published as cirrhosis hepatis teleangiectatica (Martini, 1955;Martini, 1959). One of the cases would now be classified as belonging to the CRST-syndrome (Calcinosis -Raynaudsclerodermateleangiectasia: Reynolds et al, 1971).…”

Section: Clinical Features Involvement Of Livermentioning

confidence: 99%

The liver in hereditary haemorrhagic teleangiectasia: an inborn error of vascular structure with multiple manifestations: a reappraisal.

Martini¹

1978

Gut

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“…It was consistent with the angiomatous malformations of hereditary hemorrhagic telangiectasia (Fig 1). 4. The skin and subungual lesions-unlike petechiae and splinter hemorrhages-blanched to pressure.…”

Section: Report Of Casementioning

confidence: 99%

Osler's Disease With an Aortic Arch Aneurysm

Muggia¹

1964

Arch Intern Med

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Lebercirrhose bei Morbus Osler, Cirrhosis hepatis teleangiectatica

Cited by 20 publications

References 0 publications

Cyanosis with hepatic cirrhosis: A case with pulmonary arteriovenous shunting

Cyanosis with hepatic cirrhosis: A case with pulmonary arteriovenous shunting

The liver in hereditary haemorrhagic teleangiectasia: an inborn error of vascular structure with multiple manifestations: a reappraisal.

Osler's Disease With an Aortic Arch Aneurysm

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