Atrial myxoma, a rare benign tumour of the heart, predominantly affects women in the reproductive age group. There is no consensus on the monitoring and treatment of atrial myxoma in pregnancy, as the experience is limited to a few cases reported in the literature. We report a case of a pregnant individual referred with suspected left atrial thrombus, finally diagnosed to have pedunculated left atrial myxoma and underwent successful resection along with caesarean section, resulting in good maternal–fetal outcomes.