Leiomyosarcoma of the renal vein

Abstract

The preoperative diagnosis for primary leiomyosarcoma of the renal vein, an extremely rare tumor, is difficult. The tumor predominantly occurs in women and on the left side. Its natural history is toward distant metastases and a poor 5‐year survival rate. Nephrectomy and en‐bloc surgical resection remain the mainstay of therapy. We present three such cases and review the world literature. © 1996 Wiley‐Liss, Inc.

Multidetector CT and MR Imaging Findings of Renal Vein Leiomyosarcoma with Both Extraluminal and Intraluminal Components: A Case Report

“…The inferior vena cava is responsible for more than 50% of retroperitoneal leiomyosarcoma cases (2,5). Primary leiomyosarcoma originating from the renal vein is quite uncommon with 50 to 60 years as prevalence peak age.…”

“…Primary leiomyosarcoma originating from the renal vein is quite uncommon with 50 to 60 years as prevalence peak age. It more commonly arises from the right renal vein compared to the left renal vein (2,4). Long-term outcomes are closely related to tumor size and the feasibility of complete tumor resection (5).…”

“…A leiomyosarcoma arising from the renal vein is particularly uncommon. After the first report of Varela and Garro in 1967, only about 30 cases have been reported in the published medical literature (2,3). The renal vein leiomyosarcoma is grossly classified into three subtypes: completely extravascular; completely intravascular and mixed (1,4).…”

Current view: leiomyosarcoma of the veins of the retroperitoneum. Case histories review

“…На сегодняшний день в мире описано порядка 35 случаев [17]. В целом лейомиосаркомы ПВ встречаются преимущественно слева и, как правило, у женщин в возрасте от 50 до 69 лет [18,19].…”

“…Лишь в 5 % случаев распространение на ПВ при ПКР выявляют при размере первичной опухоли < 4 см. Первичные лейомиосаркомы ПВ гораздо меньшего размера и в основном располагаются за пределами по-чек, сдавливая окружающие структуры и вызывая тем самым болевой синдром [18,21].…”