Massive rare desmoplastic fibroma of the ilium and ischium in a young adult

Abstract

Rationale:Desmoplastic fibroma (DF) is a rare, locally invasive but benign bone tumor. It represents one of the rarest bone diseases, with an incidence of only 0.11% of all primary bone tumors.Patient concerns:Herein, a case of massive and unusual DF, with simultaneous involvement of ilium and ischium, is described. A 29-year-old man suffered minor pain in his right hip for 2 years. It worsened after sudden movements, which prevented him from walking normally. Physical examination showed a limitation when the right hip was flexed and a percussion pain on the hip region. A medical imaging examination showed that the right ilium and ischium had a massive bone lesion. The top of acetabular had very little bone left and a fracture was likely at any time. No prominent body weight loss was noted, because there was no extensive invasion to the adjacent soft tissue.Diagnoses:DF of the Ilium and Ischium.Interventions:The patient underwent a surgery involving curettage and grafting to maintain the stability of the pelvis.Outcomes:The definitive pathological diagnosis was DF, without evidence of malignancy. The postoperative recovery course at 3-month follow-up was uneventful.Lessons:To the authors’ knowledge, such a massive DF involving both ilium and ischium has been rarely reported. Young patients require appropriate and timely treatment modalities.

Fibroma desmoplásico de Húmero. Reporte de caso y revisión de la literatura

“…Los sitios donde los FD se presentan con mayor frecuencia son las metáfisis de los huesos largos (58%), seguidos de la pelvis, el maxilar superior, el esternón y las vértebras 2,5 . Hasta el momento este tumor solo se ha reportado en tres informes en la diáfisis del húmero [6][7][8] .…”