Adenoid cystic carcinoma is a rare tumour accounting for less than 1% of all head and neck malignancies and 10% of all salivary gland neoplasms. 50% of cases have been found in minor salivary glands but are also reported in nose, sinuses, upper airway, lacrimal glands and breast. Those affected are in the age group 20-84 years (mean 52 years). Adenoid cystic carcinoma of the head and neck is relatively rare and is characterized by slow evolution, multiple recurrences, protracted clinical course, and late distant metastasis but frequently metastasizes to lung. Here, we are presenting a rare case of adenoid cystic carcinoma metastasizing to kidney and masquerading clinically and radiologically as primary renal cell carcinoma. Lymph node metastases are unusual, hematogenous spread, often to the lungs is quite characteristic, metastasis to kidney being extremely rare.