Motor Function Measure Scale (MFM): New Instrument for Follow-Up Brazilian Patients with Neuromuscular Disease

Iwabe, Cristina; Nucci, Anamarli; Pfeilsticker, Beatriz Helena Miranda; Magna, Luís Alberto

doi:10.5772/30752

Cited by 2 publications

(1 citation statement)

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“…These items were selected so that all participants could be tested in a similar manner, despite their level of ambulation and could be performed in approximately 10 min (Bushby & Connor 2011 ; Mazzone et al 2012 ). Each item on the MFM is scored on a four-point scale, with zero if the participant is unable to perform the task or cannot maintain the starting position whilst performing the task, and three reflects the ability to perform the task with a controlled (normal) movement pattern (Iwabe et al 2014 ; MFM user manual: https://mfm-nmd.org/obtenir-un-manuel-utilisateur/https://www.statisticshowto.datasciencecentral.com/cohens-d/ ). Therefore, in this study, participants’ MFM score was expressed out of 30, for the 10 items.…”

Section: Methodsmentioning

confidence: 99%

Inspiratory muscle training in children and adolescents living with neuromuscular diseases: A pre-experimental study

Human

Morrow

2021

South African Journal of Physiotherapy

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Background: Children with neuromuscular diseases (NMD) are at risk of morbidity and mortality because of progressive respiratory muscle weakness and ineffective cough. Inspiratory muscle training (IMT) aims to preserve or improve respiratory muscle strength, thereby reducing morbidity and improving health-related quality of life (HRQoL).Objectives: To describe the safety and feasibility of a 6-week IMT programme using an electronic threshold device (Powerbreathe®). Any adverse events and changes in functional ability, spirometry, peak expiratory cough flow (PECF), inspiratory muscle strength and HRQoL (Pediatric Quality of Life [PedsQL]) were recorded.Methods: A convenience sample of eight participants (n = 4 boys; median [interquartile range {IQR}] age: 12.21 [9.63–16.05] years) with various NMD were included in a pre-experimental, observational pre-test post-test feasibility study. Training consisted of 30 breaths, twice daily, 5 days a week, for 6 weeks.Results: There were significant pre- to post-intervention improvements in upper limb function and coordination (p = 0.03) and inspiratory muscle strength: maximum inspiratory mouth pressure (Pimax) (p = 0.01); strength-index (p = 0.02); peak inspiratory flow (PIF) (p = 0.02), with no evidence of change in spirometry, PECF or HRQoL. No adverse events occurred and participant satisfaction and adherence levels were high.Conclusion: Inspiratory muscle training (at an intensity of 30% Pimax) appears safe, feasible and acceptable, in a small sample of children and adolescents with NMD and was associated with improved inspiratory muscle strength, PIF and upper limb function and coordination.Clinical implications: Larger, longer-term randomised controlled trials are warranted to confirm the safety and efficacy of IMT as an adjunct respiratory management strategy in children with NMD.

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Section: Methodsmentioning

confidence: 99%