Multiple Intrahepatic Artery Aneurysms in a Patient with Behçet’s Disease: Use of Transcatheter Embolization for Rupture

Abstract

Intrahepatic artery aneuryms are a rare and potentially life-threatening condition. We present the first case in the English literature of multiple intrahepatic artery aneuryms in a patient with Behçet's disease who presented acutely with rupture. The ruptured aneurysm was treated successfully with transcatheter arterial coil embolization-CT and clinical follow-up confirming a good result. We discuss the management dilemma with regard to prophylactic embolization of the numerous other small asymptomatic intrahepatic aneurysms in this same patient.

Spontaneous Intra-Abdominal Hemorrhage Due to Rupture of Jejunal Artery Aneurysm in Behcet Disease

“…TCAE is indicated for both ruptured and intact aneurysms, and is considered safe and effective for arterial aneurysms in BD. 20 In our review, the success rate of TCAE was 92%. However, rupture warrants an emergent open surgery to ligation in most cases.…”

“…We diagnosed 25 patients with arterial involvement radiologically including ultrasound, 6 , 7 , 9 , 13 , 15 , 18 , 25 angiography, 8 , 9 , 13 , 14 , 16 , 18 , 19 , 24 – 28 CT, 5 , 6 , 8 , 10 – 12 , 15 , 17 , 18 , 20 – 23 , 25 – 28 and magnetic resonance angiography. 23 The most common imaging modality used was CT (76.0%) and secondary angiography (48.0%).…”

Hughes-Stovin Syndrome: An Experience of Management of 3 Cases From a Tertiary Health Care Centre

“…Involvement of left hepatic artery aneurysm in HSS patients is rare and reported only by Herb et al 13 Behcet's disease is rarely associated with hepatic artery aneurysm. [14][15][16] Also, extrapulmonary arterial involvement in HSS has been previously reported in the splenic artery, 17 internal iliac artery aneurysm, 18,19 and femoral arteries branches. 12 Optic neuritis, 20 as seen, 2 of our patients, and pan-uveitis, 21 have been previously reported in HSS.…”

Transcatheter Arterial Coil Embolization of Ruptured Common Hepatic Artery Aneurysm in a Patient with Behçet’s Disease

“…The basic pathogenesis underlying the vascular complications of Behçet's disease is vasculitis of the vasa vasorum in medium and large vessels [ 4 , 10 ]. The large arterial lesions involve inflammation of the media and adventitia.…”