Multiple stenosis of the pulmonary arteries associated with pulmonary hypertension, diagnosed by selective angiocardiography

Sarcoidosis, pulmonary hypertension, and acquired peripheral pulmonary artery stenosis

“…Peripheral pulmonary artery stenosis is usually detected in children with pulmonary hypertension and is thought to represent a congenital problem; more than half the patients have an associated congenital cardiac defect [11][12][13][14]. Although we cannot assert with absolute certainty that this present patient had acquired peripheral pulmonary artery stenosis, the development of symptoms in adulthood and the pathologic diagnosis of sarcoidosis, which responded to corticosteroid therapy, makes this seem most likely.…”

Peripheral pulmonary artery stenosis.

“…Multiple segmental stenoses of main and lobular pulmonary arteries have been identified radiologically (Arvidsson et al, 1955), and by dissection and histological examination where symmetrical reduction of the lumen to a centrally sited pin hole is described (MacMahon et al, 1967) in children with pulmonary hypertension. Multiple plexiform lesions have been described in both children and adults with pulmonary hypertension secondary to congenital heart disease and in primary hypertension (Wagenvoort and Wagenvoort, 1970).…”

Supravalvular Stenoses of the Pulmonary Arteries

“…ARVIDSSON et coll. (1) described two cases in the same family, mother and son, with multiple peripheral stenoses of the pulmonary arteries. I n 1957, VAN EPPS (21) reported two brothers with pulmonary hypertension who both had stenoses in the peripheral pulmonary arteries.…”

“…A continuous murmur occurring with isolated peripheral pulmonary stenoses has been described by several authors (1,5,8,9,18,21) and 2 patients reported (5,8) were operated on for patent ductus arteriosus before the correct diagnosis was established. None of the patients in this series with isolated peripheral stenoses had a continuous murmur.…”