Naevus flammeus im Trigeminusgebiet nach Trauma im Rahmen eines posttraumatisch-vegetativen Syndroms

Acquired Port-Wine Stain in a Pediatric Patient

“…^ Trauma-related acquired PWS has been called Fegeler syndrome, but we avoid using this term for our patient because he insistently denied any history of trauma to the site of the lesions, although he was on a rhythmic gymnastics team at school. 5 Acquired PWSs, like congenital PWSs, represent passive ectasia of cutaneous vasculature rather than active proliferation, as seen in hemangiomas.^ The pathogenesis of congenital PWS is thought to be related to a deficit of perivascular neural control, and the association of antecedent trauma can be due to trauma to the perivascular neural elements, resulting in ectasia of dermal vessels. SmoUer and Rosen suggested that an alteration in sympathetic modulation of vascular tone could play a role in the development of PWS.…”

“…1 Trauma-related acquired PWS has been called Fegeler syndrome, but we avoid using this term for our patient because he insistently denied any history of trauma to the site of the lesions, although he was on a rhythmic gymnastics team at school. 5…”

Early Morphea Mimicking Acquired Port‐Wine Stain

“…Some reports have been associated with antecedent trauma, and some cases have been thought to occur because of abnormal vascular repair . An acquired PWS that develops after obvious trauma is called Fegeler syndrome after the physician who first reported the association in 1949 . Clinically and histopathologically an acquired PWS is indistinguishable from a congenital PWS .…”

Posttraumatic Port‐Wine Stain in a 4‐Year‐Old Girl: Fegeler Syndrome

“…The first case of an acquired port‐wine stain following a trauma was reported by Fegeler in 1949 (14). Since then, trauma‐related port‐wine stain has also been called Fegeler syndrome.…”