Neurologic Involvement in Behçet's Syndrome

Pseudotumor cerebri como una manifestación excepcional de la enfermedad de Behçet: Caso clínico

“…En el caso aquí presentado el diagnóstico de su enfermedad fue simultáneo al compromiso neurológico, pero en series de neuro-Behçet esto es raro (menos del 10% de los casos), siendo lo más habitual que el compromiso neurológico aparezca entre 3 y 5 años de evolución 4,10 .…”

Beh�et's disease and late progressive myelopathy in a patient with severe kyphotic deformity following childhood spinal trauma: is there any connection?

“…From a neurological point of view, it is a systemic vasculitis that is known to cause some manifestations due to cerebral, cerebellar, brainstem, spinal cord and cranial or peripheral nerve involvement [1,7,8]. Neurological involvement in this disease, which has a benign chronic course with relapses or fluctuations, occurs in 5-50% of the patients [8].…”

“…From a neurological point of view, it is a systemic vasculitis that is known to cause some manifestations due to cerebral, cerebellar, brainstem, spinal cord and cranial or peripheral nerve involvement [1,7,8]. Neurological involvement in this disease, which has a benign chronic course with relapses or fluctuations, occurs in 5-50% of the patients [8]. While the causative role of Behçet's disease in our patient with progressive myelopathy and severe kyphotic deformity caused by spinal trauma is questionable, the mechanism of the late neurological involvement is probably "vascular" secondary to Behçet's disease rather than "mechanical" secondary to kyphosis.…”

“…Neurological problems can, on the other hand, be associated with Behçet's disease -a multisystem disease first described by the Turkish dermatologist Hulusi Behçet in 1937, with ocular, oral and genital manifestations due to a systemic vasculitis [1,7]. Neurological findings of Behçet's disease include intracranial hypertension, meningoencephalitis, and symptoms due to involvement of the peripheral or central nervous system [1,7,8]. In this study, an interesting case of a patient affected by Behçet's disease and severe kyphosis in the thoracic spine, with a history of traumatic event during childhood, is reported.…”

Clinico-Radiological Findings of Neuro-Behcet's Syndrome.

“…Approximately 5% of Behcet's syndrome patients may not develop mucocutaneous manifestations even after neurologic involvement (4,5). Previous reports have clinically determined the characteristic neurological involvement of Behcet's syndrome: brain stem type and meningoencephalitic type (6)(7)(8). However, using computed tomographic scans (CT scans), investigators often failed to detect the precise lesions corresponding to the clinical deficit.…”