Orbital lymphangiomas: clinical, radiologic, and pathologic characteristics.

Abstract

To assess the value of computed tomography (CT) in evaluation of orbital lymphangioma, the CT findings in 11 patients were retrospectively analyzed and correlated with the clinical, hemodynamic, surgical, and pathologic findings. The lesions were classified by location in three categories: superficial (n = 1), deep (n = 6), or combined (n = 6); the latter were evident earlier in life. The CT findings correlated well with the surgical and histologic findings. Orbital lymphangiomas were poorly defined lesions that crossed anatomic boundaries such as the conal fascia and orbital septum. Some degree of enhancement was the rule, ranging from scattered patchy areas to enhancement of the majority of the lesion. Areas of hemorrhage caused cystlike masses with rim enhancement. Preoperative identification of the vascular enhancing component at CT examination enables the surgeon to resect this area to prevent postoperative hemorrhage. High-resolution CT is of great value in the diagnosis and preoperative treatment planning of orbital lymphangioma.

Pediatric Orbit Tumors and Tumorlike Lesions: Nonosseous Lesions of the Extraocular Orbit

“…Those lesions that involve the superficial or anterior orbital structures are diagnosed earlier (36). Frequently, anterior lesions extend to the forehead, temporal region, and cheek (31,32,35).…”

“…When questioned, parents often recount a prior history from birth of eyelid fullness or purple discoloration of the skin, usually in the superomedial orbit (34). Vesicles may be noted in the conjunctiva, facial skin, or oral mucosa (31,32,36). Less commonly, patients present with lesions that demonstrate a more gradual growth with orbital expansion.…”

“…The latter may include expansion, remodeling, or hyperostotic or lytic lesions of the bony orbit. Some malformations extend posteriorly and widen the superior or inferior orbital fissure (26,32,36). CT is particularly sensitive for depicting the phleboliths that may be present in the venous component of these lesions (Fig 12a).…”

Sclerotherapy for Orbital Lymphangioma – Case Series and Literature Review

“…Intraorbital haemorrhage has been reported as a common cause of exacerbation of proptosis. Such haemorrhage was spontaneous, or after local/systemic infection, or local trauma (2,5,6). …”

Orbital Lymphangioma-Case Report and Review of the literature

“…Most of them presents evidence of old hemorrhageby the presence of cholesterol clefts, hemosiderin, lysed blood cells, lipid laden macrophages and foreign body reaction. Stromal components like smooth muscle fibers and loose connective tissue septa are present in varying degrees 10 .…”