Orthokeratinizing odontogenic cyst of maxilla with complex odontoma

Abstract

The orthokeratinized odontogenic cyst (OOC) and odontoma are the odontogenic cyst and tumor respectively that are minimally invasive neoplasms of head and neck region. OOC is a rare variant of odontogenic cyst characterized by the presence of excessive orthokeratin covering the cystic lining. Odontoma is a benign neoplasm/hamartoma often discovered accidently on panoramic radiographs. We came across a case of a 26-year-old male with swelling on his face along with difficulty in breathing. On the basis of radiographic and histopathological findings the final diagnosis of OOC associated with odontoma was given. However, there is no report in the English literature of the simultaneous occurrence of these two lesions and hence this case is very rare. It is unclear whether the two lesions were just coincidental or were actually related to each other.

Orthokeratinized odontogenic cyst with calcification: A rare case report of a distinct entity

“…It presents as solitary, unilocular radiolucency in the posterior mandible with cortical expansion. [ 2 3 4 ] In contrast, the present case is unique as it occurred in an 18-year-old female patient and showed calcification. Only one case has been reported till date with calcification.…”

“…[ 5 ] The recurrence rate OOC is 2.2% which is far low than that of KCOT (recurrence rate 42.6%). [ 3 15 ] Table 1 summarizes the differences between OOC and OKC.…”

Orthokeratinized Odontogenic Cyst: An Unusual Histopathological Presentation

“…Some investigators believe that OKC is a neoplasm, which they prefer to call a keratocystic odontogenic tumor (KCOT) (9). According to the WHO classification, oral cystic lesions lined by orthokeratinized epithelium are not included in the spectrum of KCOT, as the lining epithelium of OOC lacks the typical features of OKC and has lower proliferative activity (10). It has been suggested that KCOT may arise from the dental lamina, but OOC may arise from the oral epithelium under the influence of the dental papilla or only the oral epithelium (11), and for OOCs associated with an impacted tooth, a different histogenesis has been suggested (12).…”