Partial Anomalous Pulmonary Venous Return. Evaluation of 51 Cases.

Abstract

SUMMARYPartial anomalous pulmonary venous return (PAPVR) is a congenital anomaly in which one or more, but not all, of the pulmonary veins are connected to a systemic vein or to the right atrium directly. Its incidence is higher in autopsy series than in clinical series.We report 51 cases of PAPVR diagnosed by cardiac catheterization and evaluated from the aspects of age, sex, type and associated anomalies and diseases. (Jpn HeartJ 35: 43-50,1994) Key words: Partial anomalous pulmonary venous return Associated anomalies BNORMALITIES of the pulmonary venous system are not common, although their real frequency is probably greater than that deduced from clinical and autopsy studies.1) The first reported case of anomalous pulmonary venous connection was by Winslow in 1739. In 1942, Brody published a series of 106 cases.2-5) In anatomic terms, the pulmonary venous anomalies may be classified as anomalous connections, stenotic connections and abnormal numbers of pulmonary veins.1) Our subject is "Partial anomalous pulmonary venous return" defined as one or more, but not all, of the pulmonary veins being connected to the right atrium or to one or more of its tributaries. We studied 51 cases of PAPVR admitted to Hacettepe University Pediatric Cardiology Unit between 1972-1991 and diagnosed by cardiac catheterization. All patients were evaluated on the basis of age, sex, type of venous return and associated anomalies and diseases. MATERIAL AND METHODSFifty-one patients with PAPVR diagnosed by cardiac catheterization at the Hacettepe University Pediatric Cardiology Unit between 1972 and 1991 were From the

Pulmonary hypertension due to presence of isolated partial anomalous pulmonary venous connection: A case report

“…4 Most anomalous pulmonary veins arise mainly from the right lung; connecting primarily to the superior vena cava (SVC), less commonly to the right atrium (RA) or the inferior vena cava (IVC). Only 3e8% of the anomalous pulmonary veins have been reported to originate from the left lung, connecting to the left brachiocephalic vein in all cases.…”

Drenagem anômala parcial de quatro veias pulmonares com septo interatrial íntegro: relato de um caso raro

“…The interatrial septum is intact in 20% to 33% of the cases of PAPVR 1,2 . Associations with other defects occur in 20% of them.…”

“…Associations with other defects occur in 20% of them. Defects include cor triatriatum in 7.8%, mitral stenosis in 4.3% and aortic coarctation in 2.6% of the 139 cases reported from 1964 to 2006 1,2,6,7 . Other defects are sporadically associated, such as interventricular septal defect, left superior vena cava draining to the left atrium, interruption of the aortic arch, Fallot's tetralogy, atrioventricular septum defect, in addition to genetic syndromes such as the syndromes of Turner, Jarcho Levin and Kabuki 6,7 .…”

“…In partial anomalous pulmonary venous return (PAPVR), even with intact interatrial septum (from 20% to 33% of the cases), mild clinical repercussion persisted, although in the long term [1][2][3][4] .…”

“…In more than 95% of the cases of PAPVR, anomalous connections occur in one or two pulmonary veins and rarely derive from the two lungs at the same time [1][2][3][4]5 . Three and four anomalous pulmonary venous return have been reported only twice in the literature 3 .…”