Pediatric Ewing’s Sarcoma/Primitive Neuroectodermal Tumor (ES/PNET) Developed in the Small Intestine: A Case Report

Kim, You Sun; 문혜민,; 이규상,; 박영석,; young, Kim hyun; 김지영,; 조진민,; 최형수,

doi:10.15264/cpho.2017.24.2.162

Cited by 4 publications

(1 citation statement)

References 13 publications

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“…However, it is variably positive in lymphoblastic lymphoma36 In the above analysis FLI1 was not done in 18 cases (58.06%). Kim et al28 also observed that FLI1 was not done in 56% cases. Vimentin is also a useful marker and usually positive while S100, chromogranin A, synaptophysin, and neuron-specific enolase show variable sensitivity 31.…”

Section: Discussionmentioning

confidence: 98%

<p>Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation</p>

Yagnik¹,

Dawka²

2019

CEG

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Extraskeletal Ewing’s sarcoma (E-EWS)/peripheral primitive neuroectodermal tumor (pPNET) is a rare soft tissue tumor that arises from a multipotent progenitor cell and is considered to be of neuroectodermal origin. Although soft tissue E-EWS/pPNETs are common, they are exceedingly rare in the small bowel. Only 30 cases of E-EWS/pPNET of the small bowel have been reported. However, only one case of gastrointestinal perforation has been reported till today. Here, we report the second case of E- EWS/pPNET with gastrointestinal perforation.

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Section: Discussionmentioning

confidence: 98%

<p>Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation</p>

Yagnik¹,

Dawka²

2019

CEG

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Primary Ewing’s sarcoma in a small intestine – a case report and review of the literature

et al. 2020

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Background Ewing’s sarcoma usually presents in paediatric patients with its primary location being bone tissue. Nevertheless, we present such an adult case which arises from the small intestine. We registered thirty one cases of such origin published so far excluding ours. Case presentation We report a case of 30 year old female who was admitted due to the persistent anaemia. Whole body computed tomography scan revealed abdominal mass in her left upper abdominal compartment. Surgery on the mass originating from jejunum was performed, although due to extremely complicated postoperative period and rapid dissemination no additional therapy had been performed. The tumour was positive for CD99, ERG, CD56, Synaptophysin, PanCK, Cam5.2. Conclusion Extraosseus Ewing’s sarcoma is extremely rare entity, with poor prognosis.

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Primary Ewing’s sarcoma of the intestine: case report and literature review

Luo,

Gao,

et al. 2024

Front. Oncol.

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Ewing sarcoma (ES)/peripheral primitive neuroectodermal tumor is a highly aggressive malignant tumor that typically presents in bone and soft tissue. Primary ES of the intestine is relatively rare, which poses a challenge in distinguishing it from other primary tumors of the small intestine through imaging. This article details a case study of ES originating in the intestine. Computed tomography (CT) imaging suggested a small intestinal stromal tumor, and so the patient underwent resection of the small bowel and omental tumor. Pathology results confirmed the diagnosis of ES of the small intestine. Following surgery, the patient underwent six cycles of chemotherapy, and a follow-up positron emission tomography–CT revealed widespread dissemination of the disease with intraperitoneal metastasis, ultimately resulting in the death of the patient.

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Pediatric Ewing’s Sarcoma/Primitive Neuroectodermal Tumor (ES/PNET) Developed in the Small Intestine: A Case Report

Cited by 4 publications

References 13 publications

<p>Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation</p>

<p>Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation</p>

Primary Ewing’s sarcoma in a small intestine – a case report and review of the literature

Primary Ewing’s sarcoma of the intestine: case report and literature review

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