Primary Choroid Plexus Papilloma of the Cerebellopontine Angle

Abstract

W 'HILE it is not uncommon for a choroid plexus papilloma arising in the fourth ventricle to extend into the cerebellopontine angle, primary papilloma in this region is very rare2 ,~ In a detailed review of the literature, Morello and Migliavaca 4 found only nine such cases and added two cases of their own. Since then, to our knowledge, there has been no further report on primary choroid plexus papilloma in the cerebellopontine angle. This is a report of a primary cerebellopontine angle choroid plexus papilloma which was found at postmortem.Left-sided cerebellar and right-sided and cortico-spinal tract signs were also present. The routine laboratory examination was normal. Lumbar puncture revealed a pressure of 180 mm of water, 130 mg% of protein, and 45 mg% of sugar with no cells. Plain x-ray skull films did not reveal any abnormality. A right brachial angiogram was normal. Operation. A left suboccipital craniectomywas performed, and a partly cystic fairly vascular granulomatous extradural mass measuring 2.5 )< 1.5 cm was encountered. The dura appeared to be thickened. Palpa- Case ReportThis 34-year-old man was first seen in the neurological service on August 27, 1964, for left-sided facial weakness of 6 months' duration. He also complained of left-sided tinnitus, and diminished hearing. At that time, neurological examination revealed a lower motor neurone left facial weakness, left nerve deafness, and a nonfunctioning labyrinth on the left side. The patient refused admission.Examination. On December 8, 1966, the patient was admitted with difficulty in speech and swallowing. He was drowsy but cooperative, and was oriented in time and space. There was marked dysarthria. The disc margin on the right side was blurred, and the left fundus could not be seen because of severe kerato-conjunctivitis. There was bilateral lateral rectus palsy, left fifth cranial nerve palsy (both sensory and motor), left lower motor neurone facial weakness, left nerve deafness, weakness of palatal movement on the left side, and profuse discharge from the left ear.

Endolymphatic sac tumours

“…Three case reports suggest tumours arising from ectopic plexus choroideus tissue. [63][64][65] Generally, plexus papillomas grow primarily within the cranial cavity and do not invade the bone. Histologically, they are less glandular and less cystic structured.…”

Primary choroid plexus papilloma of cerebellopontine angle: An unusual entity in infancy

“…These lesions appear as multilobulated extra-axial vascular masses with a cauliflower-like appearance. [145] Differential diagnoses at this location include - acoustic schwannoma, trigeminal neuroma, ependymoma, and meningioma. While intrameatal extension is the hallmark in acoustic schwannoma, the broad dural attachment in meningioma, extension to the foramen of Luschka in ependymoma, and T1-W hyperintensity in trigeminal neuroma provide diagnostic aid for differentiation.…”