Primary Ewing’s sarcoma of the temporal bone: a rare entity and review of the literature

Abstract

Ewing’s sarcoma (ES) is the second most common malignant primary bone tumour in children and adolescents. It primarily affects the diaphysis of long bones and pelvis. ES arising from temporal bone is extremely rare. To date, 43 such cases have been described in the literature. Clinical and radiological features are non-specific. Diagnosis is based mainly on immunohistochemistry. The present article presents an extremely rare case of ES of the temporal bone in a 20-year young man, and he was successfully treated with multiagent chemotherapy and radiotherapy.

Unusual presentation of a clinically isolated temporal region mass: Non‐Hodgkin lymphoma

“…Sarcomas may be rapidly progressive depending on the subtype. Children and young adults with Ewing sarcoma of the temporal fossa present with a painful swelling, headaches, and possible facial palsy 4 …”

A Case of Ewing’s Sarcoma of the Temporal Bone in a 3-Year-Old Boy

“…Клинические и рентгенологические признаки неспецифичны. Диагноз основывается перимущественно на данных иммуногистохимии [3]. Самым молодым зарегистрированным случаем СЮ височной кости является случай саркомы Юинга височной кости у 5-месячного мальчика в 2006 г.…”