Primitive neuroectodermal adrenal gland tumour

Tsang, Yung Po; Lang, Brian HH; Tam, Siu-Cheung; Wong, KP

doi:10.12809/hkmj134127

Cited by 10 publications

(7 citation statements)

References 11 publications

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“…Existing data suggests similar outcome of adult extraosseous Ewing sarcoma compared to that of bone-confined disease in terms of response to multi-modality treatment and the prognostic factors influencing treatment success [17] , [18] . As for the field of urology, individual cases of extraosseous Ewing sarcomas have also been reported in the urinary bladder, kidneys, adrenal glands and even the penis [19] , [20] , [21] , [22] . To our knowledge only nine other cases of (peri-)prostatic Ewing sarcoma are known worldwide being first described in 2003 [23] , [24] , [25] , [26] , [27] , [28] , [29] , [30] , [31] .…”

Section: Discussionmentioning

confidence: 99%

Prostatic sarcoma of the Ewing family in a 33-year-old male – A case report and review of the literature

Esch

Barski

Bug

et al. 2016

Asian Journal of Urology

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Ewing sarcoma is the second most common primary bone tumor seen in children and adolescents, typically presenting between 10 and 20 years of age. Extraosseous sarcomas of the Ewing family in adults are rare. We report a manifestation of this tumor entity in the periprostatic tissue of a 33-year-old male and discuss our treatment approach. Transrectal biopsy is a feasible and simple diagnostic tool for unclear pelvic masses. Multi-modal therapy and central registries are needed to gain knowledge of rare pelvic tumors like Ewing sarcoma.

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Section: Discussionmentioning

confidence: 99%

Prostatic sarcoma of the Ewing family in a 33-year-old male – A case report and review of the literature

Esch

Barski

Bug

et al. 2016

Asian Journal of Urology

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“…Ewing's sarcoma/PNET of the adrenal gland is extremely rare. [1][2][3] Usually the patients present with flank pain and rapidly growing mass. USG should be done as an initial screening tool but CECT is essential to find out the relation with the surrounding structures.…”

Section: Discussionmentioning

confidence: 99%

Ewing’s Sarcoma of the Adrenal Gland

et al. 2016

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Ewing’s sarcoma (ES) or primitive neuro-ectodermal tumor (PNET) typically occurs in long or flat bones, the chest wall, extra-skeletal soft tissue, and rarely in solid organs. Incidence of adrenal Ewing’s sarcoma is very rare. Here we report a case of Ewing’s sarcoma of the right adrenal gland in an 8-year-old girl who presented with an abdominal mass. The huge tumor was managed by preoperative neo-adjuvant chemotherapy followed by surgical resection. She died due to metastasis after five months of surgery.

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“…As these tumors are considered chemo-radio-sensitive, thus adjuvant chemotherapy or radiotherapy is preconized in order to control the tumor locally and generally [10].…”

Section: Discussionmentioning

confidence: 99%

Extraskeletal Ewing's sarcoma: An adrenal localization

Batahar¹,

Elidrissi²,

Berrada³

et al. 2016

IJCRI

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International Journal of Case Reports and Images (IJCRI) is an international, peer reviewed, monthly, open access, online journal, publishing high-quality, articles in all areas of basic medical sciences and clinical specialties.Aim of IJCRI is to encourage the publication of new information by providing a platform for reporting of unique, unusual and rare cases which enhance understanding of disease process, its diagnosis, management and clinico-pathologic correlations. We report a case of a 16-year-old female who presented at our department for one month history of pleuritic chest pain. The physical examination and the thoracic radiography results supported a pleural effusion. The results of the first thoracentesis and pleural biopsy were not conclusive, thus a second thoracentesis was attempted but did not withdraw any pleural fluid. A thoracoabdominal computed tomography (CT) scan was performed which found a large infraphrenic tumor suspecting an adrenal neuroblastoma. A CT guided biopsy was done and the histopathology study revealed a malignant proliferation made of medium sized round cells. The immunohistochemistry concluded to Ewing's sarcoma. The diagnosis of primitive adrenal gland neuroectodermal tumor was established and adjuvant chemotherapy was recommended. The patient passed away during her first chemotherapy session. IJCRI publishes Conclusion:The adrenal localization of Ewing's sarcoma is rare. A neuroblastoma is the first brought up diagnosis in such presentation but an extraskeletal neuroectodermal tumor is also possible.

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Primitive neuroectodermal adrenal gland tumour

Cited by 10 publications

References 11 publications

Prostatic sarcoma of the Ewing family in a 33-year-old male – A case report and review of the literature

Prostatic sarcoma of the Ewing family in a 33-year-old male – A case report and review of the literature

Ewing’s Sarcoma of the Adrenal Gland

Extraskeletal Ewing's sarcoma: An adrenal localization

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