Proboscis Lateralis: Evaluation of the Anomaly and a Review of Two Cases

Trunklike Projection in 10-Day-Old Girl

“…An ophthalmologic examination should be done in all cases because ocular anomalies such as microphthalmia, coloboma of the eye, and lacrimal system anomalies may be found with proboscis lateralis. 3,6,7 To evaluate the intrinsic structure of the proboscis and associated anomalies and planning for surgery, CT and MRI both should be undertaken. 4 Computed tomography demonstrates details of bony anatomy.…”

“…Khoo group I proboscis lateralis is very rare, in which simple excision of the trunk may be sufficient. 7,8 However, in most cases, the reconstruction is complex and requires an otolaryngologist and ophthalmologist in addition to the reconstructive surgeon. 3 Reconstruction of the proboscis should begin as soon as the surgeon feels comfortable handling the small tissues, to minimize psychological trauma for the child and the parents.…”

“…The trunk is itself an ideal donor graft because it provides an excellent color and texture match and is lined by nasal mucosa. 1,3,7,8 Associated choanal atresia and lacrimal system anomalies should be dealt with. However, restenosis and distortion of the dacryocystorhinostomy may occur.…”

“…Selection of the surgical technique to reconstruct the proboscis should be based on the anatomical characteristics of the proboscis, its localization, and the parents' expectations. 7,8 …”

Proboscis Lateralis

“…This condition is caused by the developmental failure or absence of medial and lateral nasal processes, resulting in fusion of the maxillary process with the contralateral frontal process [1]. The various localization points of PL may be at the embryonic fusion line between the anterior maxillary process and the frontonasal process, level 1, supramedial canthal area; level 2, medial canthal area; level 3, inframedial canthal area; level 4, supranostril area ( Fig.…”