Pseudotumeur inflammatoire de l’orbite associée à une névrite optique au cours d’une maladie de Behçet

Case Report: Inflammatory orbital pseudotumor revealing Behçet's disease: an original observation

“…As orbital biopsies are rarely done, radiological diagnosis is sufficient. 7 Treatment is based on corticosteroids, [7][8][9] as is the case in our patient. However, it may be refractory to corticosteroid therapy.…”

“…5,6 It represents 4.7 to 6.3% (depending on the series) of all orbital conditions. 7 We distinguished between localized and diffuse inflammatory pseudotumors of the orbit.…”

“…It mainly affects the skeletal muscles. 7 There are few associations between orbital myositis and Behçet's disease, as mentioned in Table 1. 7,8,11,[12][13][14] It is rarely reported as an initial manifestation of Behçet's disease, as illustrated in our case.…”

“…7 There are few associations between orbital myositis and Behçet's disease, as mentioned in Table 1. 7,8,11,[12][13][14] It is rarely reported as an initial manifestation of Behçet's disease, as illustrated in our case. 7,13,14 To the best of our knowledge, this is the fourth reported case of Behçet's disease caused by an inflammatory orbital pseudotumor.…”

“…Sometimes, immunosuppressive drugs are also required. 7,15 The prognosis is favorable with this type of treatment, apart from some recalcitrant forms that require the use of TNF blockers. 16 Rituximab has demonstrated effectiveness in cases resistant to glucocorticoids, surgery, or radiation therapy.…”