Pulmonary arteriovenous malformation mimicking congenital cystic adenomatoid malformation in a newborn

Bütter, Andreana; Emran, Mohammad A.; Al‐Jazaeri, Ayman; Soglio, Dorothée Bouron‐Dal; Bouchard, Sarah

doi:10.1016/j.jpedsurg.2005.12.059

Cited by 4 publications

(9 citation statements)

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“…(53,54) The mean age at diagnosis is approximately 41 years, (55,56) and the incidence of AVM is 2-3 cases per 100,000 population. (57) Only 25-50% of patients with AVM present with signs and symptoms, which include cyanosis, digital clubbing, dyspnea, fatigue, and polycythemia.…”

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confidence: 99%

“…(57) Only 25-50% of patients with AVM present with signs and symptoms, which include cyanosis, digital clubbing, dyspnea, fatigue, and polycythemia. (53)(54)(55)(56)(57)(58) Males and females are equally likely to have an AVM. (55) Of all patients with AVM, 8-20% present with bilateral AVM, and 33-50% present with multiple AVMs, (55)(56)(57) the incidence being higher in the middle and left lower lobes ( Figure 5).…”

Section: Avmmentioning

confidence: 99%

“…(53)(54)(55)(56)(57)(58) Males and females are equally likely to have an AVM. (55) Of all patients with AVM, 8-20% present with bilateral AVM, and 33-50% present with multiple AVMs, (55)(56)(57) the incidence being higher in the middle and left lower lobes ( Figure 5). (54,57) Complications of AVMs are related to connections of the pulmonary capillary bed, with loss of the filtering function of the lung; this allows emboli and bacteria to directly exit the systemic circulation, which results in embolism or brain abscesses.…”

Section: Avmmentioning

confidence: 99%

“…Embolization and surgical resection are the principal methods for the treatment of AVM. (53,56,58) The treatment of choice for AVM is conservative lung resection; when the AVM is peripheral, wedge resection is the preferred procedure, whereas large lesions might require lobectomy or pneumonectomy, (53)(54)(55)57,59) embolization being reserved for patients in whom the surgical treatment is contraindicated or for those with multiple lesions. (53,57,58) Embolization yields excellent initial results, and resolution is achieved in 80-100% of cases; however, embolization has a high recurrence rate.…”

Section: Avmmentioning

confidence: 99%

“…(57) Of the patients with hereditary hemorrhagic telangiectasia (Osler-Weber-Rendu syndrome), 45-88% present with pulmonary AVMs. (54)(55)(56)(57) Angiography is the method of choice for the diagnosis of AVM, as well as for the delineation of the arterial supply and venous drainage of AVM. (53)(54)(55)57) More recently, three-dimensional magnetic resonance imaging has been shown to be effective and accurate in diagnosing AVM, with the advantage of being a noninvasive test.…”

Section: Final Considerationsmentioning

confidence: 99%

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Malformações pulmonares congênitas

2011

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Congenital lung malformations are rare and vary widely in their clinical presentation and severity, depending mostly on the degree of lung involvement and their location in the thoracic cavity. They can manifest at any age and can be the source of significant morbidity and mortality in infants and children. Individuals with congenital lung malformations can present with respiratory symptoms at birth or can remain asymptomatic for long periods. Recently, there has been an increase in the early diagnosis of these malformations, a change that is attributable to the routine use of prenatal ultrasound. The clinical manifestation of these malformations varies from respiratory distress in the immediate postnatal period to an incidental finding on chest X-rays. Early diagnosis and prompt treatment offer the possibility of absolutely normal lung development. The treatment of asymptomatic patients with lung malformations is controversial, because the prognosis of these diseases is unpredictable. The management of these lesions depends on the type of malformation and symptoms. Because of the risk of complications, most authors recommend resection of the lesion at the time of diagnosis. Lobectomy is the procedure of choice and yields excellent long-term results. This article describes the principal congenital lung malformations, their diagnosis, and the controversies regarding treatment.Keywords: Cystic adenomatoid malformation of lung, congenital; Bronchopulmonary sequestration; Pulmonary surgical procedures; Diagnosis. ResumoAs malformações congênitas do pulmão são raras e variam muito na sua forma de apresentação clínica e gravidade, dependendo principalmente do grau de envolvimento pulmonar e de sua localização na cavidade torácica. Elas podem se manifestar em qualquer idade e podem ser fonte de importante morbidade e mortalidade em lactentes e crianças. Os indivíduos com malformações congênitas do pulmão podem apresentar sintomas respiratórios ao nascimento, enquanto outros podem permanecer assintomáticos por longos períodos. Atualmente, com o uso rotineiro da ultrassonografia pré-natal, vem ocorrendo um aumento no diagnóstico mais precoce dessas malformações. A manifestação clínica dessas malformações varia desde uma disfunção respiratória pós-natal imediata a um achado acidental na radiografia de tórax. O diagnóstico precoce e o tratamento imediato oferecem a possibilidade de um desenvolvimento pulmonar absolutamente normal. Quando assintomáticos, a conduta para o tratamento dos pacientes com malformações pulmonares ainda é controversa, uma vez que o prognóstico dessas afecções é imprevisível. O manejo dessas lesões depende do tipo de malformação e de sintomas. Devido ao risco de complicação, a maioria dos autores sugere a ressecção da lesão no momento em que essa é identificada. A lobectomia é o procedimento de escolha, fornecendo excelentes resultados a longo prazo. Este artigo descreve as principais malformações pulmonares congênitas, seu diagnóstico e controvérsias quanto o tratamento. (5) is covered by ...

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Section: Avmmentioning

confidence: 99%

Section: Avmmentioning

confidence: 99%

Section: Avmmentioning

confidence: 99%

Section: Avmmentioning

confidence: 99%

Section: Final Considerationsmentioning

confidence: 99%

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Malformações pulmonares congênitas

2011

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Congenital Chest Malformations: A Multimodality Approach with Emphasis on Fetal MR Imaging

Daltro¹,

Werner²,

Gasparetto³

et al. 2010

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Congenital chest malformations can range from small and asymptomatic entities to large space-occupying masses that require immediate surgical treatment. They may affect the foregut, pulmonary airway, and vasculature. Hybrid conditions are commonly seen, with interrelated chest malformations having various radiologic and pathologic features. An understanding of the in utero complications associated with fetal chest masses is essential for appropriate monitoring during pregnancy, treatment recommendations, and delivery management. Technologic advances have greatly improved the diagnosis of fetal anomalies. Congenital chest malformations are usually evaluated in the prenatal period with fetal sonography, but fetal magnetic resonance (MR) imaging is a well-established modality that is used as an adjunct technique in difficult diagnostic situations. MR imaging can provide excellent tissue contrast with more accurate analysis of the fetal anatomy and superior differentiation between the abnormalitites and adjacent structures, thereby allowing early planning of prenatal management.

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Early neonatal complications from pulmonary arteriovenous malformations in hereditary hemorrhagic telangiectasia: case report and review of the literature

Gludovacz

Vlasselaer

Mesens

et al. 2011

The Journal of Maternal-Fetal & Neonatal Medicine

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Hereditary hemorrhagic telangiectasia (HHT) is a rare but life-threatening disease characterized by multi system telangiectasias and arteriovenous malformations (AVM). Complications in adults have been reported extensively, but neonatal (NN) complications have only been published in incidental case reports. In this paper, we present a literature review on NN pulmonary AVM related to HHT, following our own experience with a NN death due to this disease. As prenatal diagnosis of pulmonary AVM is feasible, we recommend that a family history of HHT should be an indication for expertise prenatal anomaly scanning, in order to organise optimal NN support at birth.

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Pulmonary arteriovenous malformation mimicking congenital cystic adenomatoid malformation in a newborn

Cited by 4 publications

References 4 publications

Malformações pulmonares congênitas

Malformações pulmonares congênitas

Congenital Chest Malformations: A Multimodality Approach with Emphasis on Fetal MR Imaging

Early neonatal complications from pulmonary arteriovenous malformations in hereditary hemorrhagic telangiectasia: case report and review of the literature

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