1994
DOI: 10.1177/000331979404500508
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Pulmonary Artery Aneurysm Due to Severe Congenital Pulmonic Stenosis

Abstract: Although dilatation of the pulmonary artery (PA) is characteristic of pulmonic valve stenosis (PVS), the occurrence of a PA aneurysm in association with PVS is very rare. The authors describe a patient with severe, dome-shaped PVS who developed a 6.5 cm pulmonary trunk aneurysm. Long-term follow-up after surgical valvotomy demonstrated that the size of the aneurysm remained unchanged. Pertinent literature and implications on the natural history and management of these aneurysms are discussed.

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Cited by 47 publications
(24 citation statements)
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“…The patient died of heart failure 7 years after the operation, yet the aneurysm had not expanded postoperatively, suggesting that the prognosis of some patients with pulmonary artery trunk aneurysms is relatively benign, particulary in the absence of left-to-right shunting and significant pulmonary hypertension. 9 Garcia-Rinardi et al reported that no recurrence of aneurysm was found 6 years after aneurysmorrhaphy and closure of a ventricular septal defect. '° In our case, no evidence of recurrence of pulmonary artery aneurysm exists 3 years after operation.…”
Section: Discussionmentioning
confidence: 98%
“…The patient died of heart failure 7 years after the operation, yet the aneurysm had not expanded postoperatively, suggesting that the prognosis of some patients with pulmonary artery trunk aneurysms is relatively benign, particulary in the absence of left-to-right shunting and significant pulmonary hypertension. 9 Garcia-Rinardi et al reported that no recurrence of aneurysm was found 6 years after aneurysmorrhaphy and closure of a ventricular septal defect. '° In our case, no evidence of recurrence of pulmonary artery aneurysm exists 3 years after operation.…”
Section: Discussionmentioning
confidence: 98%
“…In 2004, Loukas et al [2 ]reported a case of Noonan’s syndrome with pulmonary valvular stenosis and coronary aneurysms, and in 2005, Purnell et al [3] reported a case of Noonan’s syndrome with giant aneurysms of the sinuses of Valsalva and aortic regurgitation; however, there have been no published reports of pulmonary artery aneurysms in association with this disease. In fact, the occurrence of a pulmonary artery aneurysm in the setting of pulmonary valve stenosis is very rare [4]. …”
Section: Discussionmentioning
confidence: 99%
“…1,2 Congenital pulmonic valve stenosis is associated with pulmonary artery dilation, but true pulmonary artery aneurysm formation in this clinical situation is rarely reported in the literature. 3 Proximal pulmonary artery aneurysm is usually defined by one of two main criteria: the PA/aorta diameter ratio greater than 2 as seen on transthoracic echocardiography 3,2 or a pulmonary artery diameter of greater than either 4 cm 4,5 or 5 cm 3 . On CT scans of adults, the upper limit of normal for the main PA diameter is 2.9 cm, which is another measurement used as the cutoff for pulmonary artery aneurysm.…”
Section: Schwalk Et Al Pulmonary Artery Aneurysm Secondary To Congenmentioning
confidence: 99%