Pulmonary Sequestration — A Review of 8 Cases Treated with Lobectomy

Pikwer, Andreas; Gyllstedt, Erik; Lillo-Gil, Ramon; Jönsson, Per; Guðbjartsson, Tómas

doi:10.1177/145749690609500312

Cited by 29 publications

(20 citation statements)

References 22 publications

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“…Pulmonary sequestration is a congenital malformation of unknown aetiology where non-functioning lung tissue lacks communication with the tracheobronchial tree and draws its blood supply from the systemic circulation 3 4. The condition is rare and accounts for <1 in 10 of all congenital pulmonary anomalies 5…”

Section: Discussionmentioning

confidence: 99%

Rare case of haemoptysis

Awouda¹,

Elnori

Ahmed

2017

BMJ Case Reports

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We report a case of a 39-year-old man who presented with coughing up blood for 5 days. On the day of admission, he coughed up about 300 mL of fresh blood. He mentioned that he has had cough for the past 10 years. On clinical examination, he was afebrile, tachypneic, tahycardic and normotensive. Rest of the physical examination was normal. His oxygen saturation breathing room air was 96%. His full blood count showed haemoglobin 9.3 g/dL. His chest radiograph was reported as normal. CT chest showed a vascular right paracardiac soft tissue density. On the basis of this, a diagnosis of pulmonary sequestration was considered. CT angiography of the soft tissue density identified multiple sources of systemic arterial blood. Two arteries were arising from the descending aorta and a third artery was coming from the right renal artery. Surgical removal of the sequestrated lobe was performed. The patient has an uneventful postoperative recovery and remained well at follow-up 2 months after surgery.

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Section: Discussionmentioning

confidence: 99%

Rare case of haemoptysis

Awouda¹,

Elnori

Ahmed

2017

BMJ Case Reports

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“…ELS presents mostly in the first 6 months of life with acute respiratory distress or feeding difficulties. 60% of children with ELS have co-existent congenital malformations including diaphragmatic hernia, congenital heart disease, scimitar syndrome, congenital cystic adenomatoid malformation (CCAM) or lung hypoplasia (1,7).…”

Section: Discussionmentioning

confidence: 99%

Intralobar Bronchopulmonary Sequestration with Mixed Venous Drainage in a 10-Year-Old Girl

Boetzkes

Wojciechowski

Beukelaar

et al. 2009

Acta Chirurgica Belgica

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Bronchopulmonary sequestration consists of a mass of abnormal lung tissue that has no normal connection with the bronchial tree and is supplied with blood from an aberrant artery mostly originating in the thoracic aorta. Two forms are recognized: intralobar and extralobar sequestration. The first is localized within the normal visceral pleura and has a venous drainage into the pulmonary system; the latter is localized without the normal lung in its own pleura with venous drainage into the systemic venous system. Intralobar sequestration is the most common form accounting for 75% of the cases. Intralobar sequestration usually presents in adolescence or adulthood with signs of recurrent pneumonia. Extralobar sequestration presents early in life with respiratory distress or feeding difficulties and is frequently associated with other congenital malformations. The diagnosis is confirmed by CT scan of the lungs and magnetic resonance angiography as demonstration of the aberrant vascular supply is essential for the diagnosis. Therapy consists in surgical removal. We present a case of intralobar sequestration in a 10-year-old girl. The clinical symptomatology was typical. Arterial supply with two aberrant arteries and mixed venous drainage into the pulmonary and systemic systems were particular features.

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“…2,4,5,7,10,15,20 Because of the wide range of symptoms at clinical onset, the diagnosis may be difficult, especially in children and young adults with concomitant congenital heart lesions. [2][3][4][5]32,33 Pulmonary artery hypertension often occurs and is seen mostly in infants 12,14,16 -18,20 with associated congenital heart malformations or with an anomalous large systemic arterial supply. 11,34 -37 However, it has also been reported in adult patients.…”

Section: Discussionmentioning

confidence: 99%

“…1,10,11,15,20 This syndrome can present early in the neonatal period or later in life with a wide clinical spectrum. 4,14,16,21 Dupuis et al 19 divided scimitar syndrome into 3 main forms: an infantile form with symptoms and pulmonary hypertension, an "older" adult form distinguished by being asymptomatic in infancy, and a form with associated congenital cardiac anomalies.…”

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confidence: 99%

“…4,13 Several different surgical approaches have been described over the years and are currently used, depending on the anatomic and pathological features of each case and according to the surgeon's preference. 15,19 -28 The objective of this study was to analyze the surgical results and follow-up outcome of patients who underwent surgery for scimitar syndrome within a European Congenital Heart Surgeons Association (ECHSA) multicentric data collection in a relatively recent time period.…”

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confidence: 99%

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Scimitar Syndrome

Vida¹,

Padalino²,

Boccuzzo³

et al. 2010

Circulation

140

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Background— Scimitar syndrome is a rare congenital heart disease. To evaluate the surgical results, we embarked on the European Congenital Heart Surgeons Association (ECHSA) multicentric study. Methods and Results— From January 1997 to December 2007, we collected data on 68 patients who underwent surgery for scimitar syndrome. Primary outcomes included hospital mortality and the efficacy of repair at follow-up. Median age at surgery was 1.4 years (interquartile range, 0.46 to 7.92 years). Forty-four patients (64%) presented with symptoms. Surgical repair included intraatrial baffle in 38 patients (56%; group 1) and reimplantation of the scimitar vein onto the left atrium in 21 patients (31%; group 2). Eight patients underwent right pneumectomy, and 1 had a right lower lobe lobectomy (group 3). Four patients died in hospital (5.9%; 1 patient in group 1, 2.6%; 3 patients in group 3, 33%). Median follow-up time was 4.5 years. There were 2 late deaths (3.1%) resulting from severe pulmonary arterial hypertension. Freedom from scimitar drainage stenosis at 13 years was 83.8% in group 1 and 85.8% in group 2. Four patients in group 1 were reoperated, and 3 patients (2 in group 1 [6%] and 1 in group 2 [4.8%]) required balloon dilation/stenting for scimitar drainage stenosis. Conclusions— The surgical treatment of this rare syndrome is safe and effective. The majority of patients were asymptomatic at the follow-up control. There were a relatively high incidence of residual scimitar drainage stenosis that is similar between the 2 reported corrective surgical techniques used.

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Pulmonary Sequestration — A Review of 8 Cases Treated with Lobectomy

Cited by 29 publications

References 22 publications

Rare case of haemoptysis

Rare case of haemoptysis

Intralobar Bronchopulmonary Sequestration with Mixed Venous Drainage in a 10-Year-Old Girl

Scimitar Syndrome

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