Pulmonary vascular disorders masquerading as interstitial lung disease

Sondheimer, Henry M.; Lung, Maky; Brugman, Susan M.; Iklé, David; Fan, Leland L.; White, Carl W.

doi:10.1002/ppul.1950200505

Cited by 36 publications

(26 citation statements)

References 34 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Because PVD can masquerade as diffuse lung disease, 540 screening for PAH in all infants and children with these diseases is clinically indicated. Furthermore, the presence of PAH in patients with interstitial lung disease is associated with a worse prognosis.…”

Section: Lung Diseasesmentioning

confidence: 99%

Pediatric Pulmonary Hypertension

Abman¹,

Hansmann²,

Archer³

et al. 2015

Circulation

949

405

View full text Add to dashboard Cite

Abstract-Pulmonary hypertension is associated with diverse cardiac, pulmonary, and systemic diseases in neonates, infants, and older children and contributes to significant morbidity and mortality. However, current approaches to caring for pediatric patients with pulmonary hypertension have been limited by the lack of consensus guidelines from experts in the field. In a joint effort from the American Heart Association and American Thoracic Society, a panel of experienced clinicians and clinician-scientists was assembled to review the current literature and to make recommendations on the diagnosis, evaluation, and treatment of pediatric pulmonary hypertension. This publication presents the results of extensive literature reviews, discussions, and formal scoring of recommendations for the care of children with pulmonary hypertension. Key Words: AHA Scientific Statements ◼ bronchopulmonary dysplasia ◼ congenital diaphragmatic hernia ◼ congenital heart disease ◼ genetics ◼ persistent pulmonary hypertension of the newborn ◼ sickle cell disease © 2015 by the American Heart Association, Inc., and the American Thoracic Society.Circulation is available at http://circ.ahajournals.org DOI: 10.1161/CIR.0000000000000329 †Deceased. The American Heart Association and the American Thoracic Society make every effort to avoid any actual or potential conflicts of interest that may arise as a result of an outside relationship or a personal, professional, or business interest of a member of the writing panel. Specifically, all members of the writing group are required to complete and submit a Disclosure Questionnaire showing all such relationships that might be perceived as real or potential conflicts of interest.This document was approved by the American Heart Association Science Advisory and Coordinating Committee on May 12, 2015, the American Heart Association Executive Committee on July 22, 2015, and the American Thoracic Society on July 24, 2015.The online-only Data Supplement is available with this article at http://circ.ahajournals.org/lookup/suppl/doi:10.1161/CIR.0000000000000329/-/DC1. The American Heart Association requests that this document be cited as follows: Abman SH, Hansmann G, Archer SL, Ivy DD, Adatia I, Chung WK, Hanna BD, Rosenzweig EB, Raj JU, Cornfield D, Stenmark KR, Steinhorn R, Thébaud B, Fineman JR, Kuehne T, Feinstein JA, Friedberg MK, Earing M, Barst RJ, Keller RL, Kinsella JP, Mullen M, Deterding R, Kulik T, Mallory G, Humpl T, Wessel DL; on behalf of the American Heart Association Council on Cardiopulmonary, Critical Care, Perioperative and Resuscitation, Council on Clinical Cardiology, Council on Cardiovascular Disease in the Young, Council on Cardiovascular Radiology and Intervention, Council on Cardiovascular Surgery and Anesthesia, and the American Thoracic Society. Pediatric pulmonary hypertension: guidelines from the American Heart Association and American Thoracic Society. Circulation. 2015;132:2037-2099 Copies: This document is available on the World Wide Web site of the American Heart Associat...

show abstract

Section: Lung Diseasesmentioning

confidence: 99%

Pediatric Pulmonary Hypertension

Abman¹,

Hansmann²,

Archer³

et al. 2015

Circulation

949

405

View full text Add to dashboard Cite

show abstract

“…Arterial, venous, or lymphatic abnormalities masquerading as ILD by clinical and imaging criteria are known to account for a proportion of cases that come to lung biopsy (36). Of the nine cases in this category, six had a clinical diagnosis of pulmonary hypertension; however, five biopsies were performed for unexplained diffuse lung disease, while vascular abnormalities were suspected in four biopsies obtained at the time of cardiac repair.…”

Section: Disorders Masquerading As Ildmentioning

confidence: 99%

Diffuse Lung Disease in Young Children

Deutsch

Young

Deterding

et al. 2007

Am J Respir Crit Care Med

Self Cite

448

191

View full text Add to dashboard Cite

“…The trend toward worsening or improvement, age at presentation, immunocompetence, and family history (i.e., whether there are other family members with adult ILD, chILD diagnoses, or a history of neonatal respiratory failure) are also important factors (10,(21)(22)(23)(24). Regarding disease severity, this judgment may be based upon the degree of symptoms (25) and gas exchange abnormalities, or the presence of echocardiographic evidence of pulmonary hypertension (26). Imaging studies can demonstrate the distribution and extent of disease, but may not correlate with functional severity, response to therapy, or prognosis.…”

Section: Diagnostic Evaluation Overviewmentioning

confidence: 99%

“…The observations described here derive from a multicenter retrospective study (6), one single-center retrospective case series study (25), and two single-center prospective case series (13,26) that evaluated the prevalence of congenital cardiac and vascular disorders in children suspected of having ILD, as well as two diagnostic accuracy studies for echocardiographic evaluation of pulmonary hypertension in adults with DLDs (27,28). The studies also reported that pulmonary vascular disease negatively affects survival in children with ILD, a finding that is comparable to the negative prognosis of adults with pulmonary hypertension and ILD (29)(30)(31)(32).…”

Section: Diagnostic Testsmentioning

confidence: 99%