Pulmonary Vein Stenosis in a Newborn: A Commonly Overlooked Diagnosis

Bravo-Valenzuela, Nathalie Jeanne; Silva, Guilherme Ricardo Nunes; Varella, Marcela Pinto

doi:10.1155/2015/870257

Cited by 4 publications

(5 citation statements)

References 11 publications

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“…However, in the literature, the definition of PVO is not precise. Some of the authors define PVO as a PV flow velocity accelerated >2.5 m/s [ 12 ], >1.6 m/s [ 29 , 30 ], while some define it as >1.1 m/s [ 31 ]. On the other hand, in normal healthy children, we do not observe PV flow >1 m/s [ 32 ].…”

Section: Discussionmentioning

confidence: 99%

Surgical Outcomes of Total Anomalous Pulmonary Venous Connection Repair

Jaworski

Kansy

Friedman-Gruszczyńska

et al. 2022

Medicina

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Background and Objectives: Over the years, surgical repair of total anomalous pulmonary venous connection (TAPVC) outcomes have improved, however, morbidity and mortality still remain significant. This study aims to assess the early and long-term outcomes of surgical treatment of TAPVC children, operated on between 2006 and 2016, in one pediatric center in Poland. Materials and Methods: Diagnostics, surgical treatment, and follow-up data from 83 patients were collected. In addition, survival and risk factor analyses, control echocardiographic, and electrocardiographic examinations were performed. Results: In the analyzed group (n = 83), there were seven hospital deaths (within 30 days after the operation) (8.4%) and nine late deaths (10.8%). The mean follow-up time was 5.5 years, and, for patients who survived, it was 7.1 years. The mean survival time in patients with completed follow-up (n = 70) was 10.3 years; the overall five-year survival rate was 78.4%. Independent mortality risk factors were type I TAPVC, single ventricle physiology, time from admission to operation, intensive care unit stay, postoperative hospital stay, and temporary kidney insufficiency requiring dialysis. Conclusions: The presence of single ventricle physiology and the supracardiac subtype of TAPVC might be negative prognostic factors, while normal heart physiology presents with good post-repair results. This study indicates that cardiac arrhythmias may occur. Morbidity and mortality, related to surgical TAPVC correction, still remain significant.

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Section: Discussionmentioning

confidence: 99%

Surgical Outcomes of Total Anomalous Pulmonary Venous Connection Repair

Jaworski

Kansy

Friedman-Gruszczyńska

et al. 2022

Medicina

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“…Approximately 50% of patients with primary PVS have other congenital heart defects (CHD), mostly septal defects. 12 Primary PVS has also been associated with bronchopulmonary dysplasia (BPD) and preterm birth. 10,11 In one case study of a consanguineous Turkish family of four siblings with primary PVS, it was associated with antenatally detected lymphatic abnormalities.…”

Section: Discussionmentioning

confidence: 99%

“…Patients usually become symptomatic in the first months to years of life. Approximately 50% of patients with primary PVS have other congenital heart defects (CHD), mostly septal defects 12 . Primary PVS has also been associated with bronchopulmonary dysplasia (BPD) and preterm birth 10,11 .…”

Section: Discussionmentioning

confidence: 99%

Left hypoplastic lung and hemoptysis—rare familial unilateral pulmonary vein atresia

Cohn

Hicks

Lacson

et al. 2020

Clinical Case Reports

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“…Pulsed Doppler with monophasic pulmonary venous flow and peak velocities >1.6 m/s are suggestive of pulmonary vein stenosis. 2 Pulmonary vein stenosis is related to prematurity and CHD due to large left-to-right shunts (ex. patent ductus arteriosus, atrial/ventricular septal defects).…”

Section: Discussionmentioning

confidence: 99%

“…1 About half of the patients have some other form of CHD, which makes the assessment of the pulmonary veins important in patients with CHD. 2 The severity and timing of the clinical presentation are linked to the number of veins involved and the degree of obstruction. Depending on disease severity, patients often present in the first months/years of life with signs of congestive heart failure and/or pulmonary hypertension.…”

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confidence: 99%