Quadricuspid Aortic Valve

Moraru, Aurelian Corneliu; Ceomîrtan-Negrii, Ioana Maria; Floria, Mariana

doi:10.2478/inmed-2020-0119

Cited by 1 publication

(1 citation statement)

References 4 publications

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“…A 64-year-old woman with past medical history (PMH) of severe AR presenting with fatigue, dyspnea, and palpitations was found to have QAV and underwent valvular replacement [ 18 ]. A 34-year-old man presenting with progressive dyspnea was found to have QAV associated with moderate AR on TTE and underwent symptomatic medical treatment [ 19 ]. Unlike our patient who had QAV with severe aortic and mitral regurgitation and a dilated ascending aorta, these case reports portrayed patients with pure AR which is known to be the most prevalent anomaly associated with QAV.…”

Section: Discussionmentioning

confidence: 99%

A Congenital Quadricuspid Aortic Valve Associated With Aortic and Mitral Regurgitation: Case Report and Literature Review

Shadman¹,

Asadi²,

Nomigolzar³

et al. 2021

Cureus

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Quadricuspid aortic valve (QAV) is a rare congenital cardiac anomaly that commonly becomes symptomatic in the fifth or sixth decade of life and can present as an isolated finding or in association with other congenital cardiovascular abnormalities. Previously, QAV was mainly a postmortem or intraoperative diagnosis and data was very limited on its natural history, associated complications, and long-term outcomes. In recent decades, however, there has been an increase in the reported cases of QAV, considering the advances in the diagnostic modalities such as transthoracic echocardiography (TTE), transesophageal echocardiography (TEE), and cardiac magnetic resonance (CMR). In this article, we present a case of a congenital QAV associated with aortic regurgitation as well as briefly review the QAV classification systems, treatment options, and long-term outcomes. A 48-year-old woman with a significant past medical history (PMH) of hypertension and coronary artery disease presented with shortness of breath, chest pain, and orthopnea for two to three weeks. The patient’s TTE showed severe aortic regurgitation with significant compromise in cardiac output that could not be otherwise explained. Subsequently, her TEE revealed QAV as the underlying source of these findings. Although the diagnosis of QAV could be very challenging, it is crucial to be considered when evaluating a patient with inscrutable progressive aortic regurgitation. Today, as a result of technological advancement, QAV is being diagnosed more accurately and promptly. Since there are no universal guidelines defined for this cardiac anomaly, regular follow-up with these patients is imperative to monitor for early signs of valvular compromise and to treat accordingly through medical and surgical interventions.

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Section: Discussionmentioning

confidence: 99%