Results of Retinal Detachment Surgery in Marfan Syndrome in Asians

Abstract

With appropriate surgical intervention, an excellent anatomic reattachment rate and good visual outcome can be achieved in Marfan syndrome patients with retinal detachment regardless of their lens status.

Risk factors for postoperative complications in lensectomy–vitrectomy with or without intraocular lens placement in ectopia lentis associated with Marfan syndrome

“…Ectopia lentis and zonular deficiency are assumed to result in a constant pull on the ora serrata, liquefied and mobile vitreous gel, traction on vitreoretinal adhesion, and increased axial length, thus causing retinal thinning and predisposing these eyes to RD 14 15. Comparing the characteristics between those patients with detached and non-detached retinas in our study, a more severe grade of lens dislocation and more high axial myopia were detected in those with detached retinas.…”

Ageing in Marfan syndrome

“…Lee and Ang (24) noted a much higher frequency of retinal detachment in MFS male patients when compared with female patients (11 : 1) in an Asian population retrospectively observed over a 10‐year period; Abboud (25) found a similar ratio (13 : 1) in a study performed in Saudi Arabia. This was not supported by our data, where seven male and seven female patients had experienced retinal detachment.…”

Surgery for Pediatric Vitreoretinal Disorders

“…112 The edge of the clear or cataractous subluxated lens hampers evaluation of the peripheral fundus. 112 The edge of the clear or cataractous subluxated lens hampers evaluation of the peripheral fundus.…”

“…112 But poorer visual outcome is likely to be encountered when there is concomitant lens dislocation or a history of intraocular surgery. Generally, the results are comparable with those patients without Marfan syndrome and successful reattachment of the retina is achieved in 86% 113 to 100%.…”

“…Generally, the results are comparable with those patients without Marfan syndrome and successful reattachment of the retina is achieved in 86% 113 to 100%. 111,112 Congenital X-linked retinoschisis Congenital X-linked retinoschisis (CX-LRS) is an inherited retinal disease characterized by abnormal Müller's cell pillars that allow schisis cavities to form. 112 The increased incidence of high myopia and peripheral lattice degeneration predisposes these eyes to retinal breaks.…”