Retroperitoneal fibrosis and juvenile rheumatoid arthritis

Abstract

We describe a 13-year-old girl with juvenile rheumatoid arthritis who developed obstructive uropathy and renal failure. Retroperitoneal fibrosis (RPF) was confirmed by surgery. Although the renal failure and hydronephrosis resolved after surgery, the symptoms of vascular occlusion persisted. We consider that early diagnosis and treatment are essential. In cases of autoimmune disease, RPF should be considered when there is acquired obstructive uropathy accompanied by vascular occlusion syndrome.

Chronic Periaortitis as a Systemic Autoimmune Disease

“…Chronic periaortitis may frequently be associated with fibroinflammatory disorders affecting other organs, IgG4-related systemic disease, which have an autoimmune origin (Matsumoto et al, 2008;Ito et al, 2008;Kasashima et al, 2008;Sakata et al, 2008). Other rheumatic diseases reported in patients with chronic periaortitis include ankylosing spondylitis, juvenile rheumatoid arthritis, systemic lupus erythematosus and antiphospholipid syndrome (Leblanc et al, 2002;Tsai et al, 1996;Okada et al, 1999;Kim et al, 2010).…”