Right Pulmonary Artery-to-Left Atrial Fistula: A Rare Cause of Neonatal Cyanosis

Kumar, Saktheeswaran Mahesh; Sivasubramonian, Sivasankaran

doi:10.1007/s00246-012-0534-y

Cited by 4 publications

(3 citation statements)

References 5 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…On the other hand, based on our review of the literature, shunts as small as 7 mm can cause paradoxical brain embolism 2 6 , 9 – 11 The present case is the first documentation of an adolescent presenting with a renal thromboembolic event due to a pulmonary arteriovenous fistula.…”

mentioning

confidence: 71%

Renal thromboembolism from a large pulmonary artery to a pulmonary vein fistula in an asymptomatic adolescent

2016

View full text Add to dashboard Cite

Pulmonary arteriovenous fistula is a rare vascular anomaly that can cause significant morbidity and mortality. The presence and significance of symptoms are dependent on the size of the right-to-left shunt. Thromboembolic events may result in cerebrovascular accidents or systemic vascular occlusions. We present a case of an adolescent without cardiorespiratory symptoms, who developed flank pain due to renal infarction, followed by a brief literature review.

show abstract

mentioning

confidence: 71%

Renal thromboembolism from a large pulmonary artery to a pulmonary vein fistula in an asymptomatic adolescent

2016

View full text Add to dashboard Cite

show abstract

“…The action of branches as direct right‐to‐left shunts results in central cyanosis, clubbing, exertional dyspnea, and polycythemia, when the shunts are large. Cyanosis is an outstanding feature of the entity but occasionally appears after birth . Symptoms depend on the size and location of the fistula.…”

Section: Discussionmentioning

confidence: 99%

Fistula between the right pulmonary artery and the left atrium coexisting with a secundum‐type atrial septal defect: An unusual case of cyanosis in a girl

et al. 2019

View full text Add to dashboard Cite

A fistula between the pulmonary artery (PA) and the left atrium (LA) is a rare congenital heart disease that usually presents with cyanosis, clubbing, and dyspnea, as well as the signs and symptoms of a right‐to‐left shunt. Herein, we report a 16‐year‐old girl with a fistula between the right PA and the LA. This type of fistula could lead to systemic desaturation. This patient also had an atrial septal defect of the secundum type and has been followed up without treatment. The clinical manifestations and treatment of fistulas located between the PA and LA are also reviewed in this report.

show abstract

“…To our knowledge, there have been 17 reported cases of RPA-LA fistula diagnosed in neonates since 1976 (Table 1). 2,[5][6][7][8][9][10][11][12][13][14][15][16][17] One patient was successfully managed nonoperatively, 11 four underwent transcatheter closure, 8,10,14,16 one was still awaiting percutaneous closure, 13 one died before surgical intervention, 6 and seven (70%) of the ten neonates (including the present case) survived operative repair. 7,9,12,15,17 We report the case of a newborn infant with an RPA-LA fistula who was successfully treated by ligation and division on cardiopulmonary bypass.…”

Section: Introductionmentioning

confidence: 99%

Right Pulmonary Artery to Left Atrial Fistula in a Neonate

Mongé

Russell

Popescu

et al. 2014

World J Pediatr Congenit Heart Surg

View full text Add to dashboard Cite

A communication between the right pulmonary artery (RPA) and the left atrium is a rare congenital anomaly that presents with cyanosis and heart failure. We describe the surgical repair of an RPA to left atrial fistula using cardiopulmonary bypass in a neonate. Advanced imaging (computed tomography scan) guided the surgical approach. Although previous reports have associated a patent ductus arteriosus with high neonatal mortality, in our case, the ductus arteriosus was actually important for maintaining enough total pulmonary blood flow.

show abstract

Right Pulmonary Artery-to-Left Atrial Fistula: A Rare Cause of Neonatal Cyanosis

Cited by 4 publications

References 5 publications

Renal thromboembolism from a large pulmonary artery to a pulmonary vein fistula in an asymptomatic adolescent

Renal thromboembolism from a large pulmonary artery to a pulmonary vein fistula in an asymptomatic adolescent

Fistula between the right pulmonary artery and the left atrium coexisting with a secundum‐type atrial septal defect: An unusual case of cyanosis in a girl

Right Pulmonary Artery to Left Atrial Fistula in a Neonate

Contact Info

Product

Resources

About