Ross syndrome, an entity included within the spectrum of partial disautonomic syndromes

Abstract

Ross syndrome is a degenerative peripheral nervous system disorder defined by the following triad: unilateral or bilateral segmental anhidrosis, hyporeflexia of deep tendon reflexes and Adie's tonic pupils. The most disturbing symptom is segmental compensatory hyperhidrosis. It has only occasionally been reported in the dermatological literature. We present a 35-year-old woman with chronic hepatitis C who developed the characteristic triad of Ross syndrome within 1 month. The patient was otherwise healthy except for an aneurysm of the left medium brain artery not responsible for the syndrome.

Ross Syndrome with Sweating Anomaly Associated with Sjögren Syndrome: An Infrared Thermo­graphic Case Study

“…However, as reported in several studies, the main objective symptoms were the concomitant presence of a well-delimited compensatory hyperhidrosis and a disabling heat intolerance (1,5,6). Ross syndrome is considered as the expression of an unknown injury to the peripheral autonomie nervous system (7).…”

Diseases of cutaneous appendages

“…1522 It has been reported dysplasia (see p. 276), 1466 but a rare acquired form has been reported. Eccrine ductal mucinosis refers to the accumulation of mucin between the cells of the outer layers of the eccrine duct.…”

Ross syndrome

“…The anhidrosis may be localized or widespread. [5] Our patient had typical areas of hypohidrosis and compensatory hyperhidrosis with weak tendon reflexes and tonic pupil. [2] Cardiac sympathetic denervation that may be asymptomatic has been shown to develop.…”