Sacro-Coccygeal Chordoma. A Review and Presentation of Three Additional Cases

Chordoma:A Clinicopathologic and Prognostic Study of a Swedish National Series

“…Extensive reviews and studies of chordoma have been published since 1894 when Ribbert gave the tumor its name; since then at least 700 cases of chordoma have been reported (although it is obvious that many reports and reviews deal with the same chordomas). The tumor is most often located in the sacrococcygeal area (approximately 50 per cent), somewhat less commonly in the spheno-occipital area (approximately 35 per cent) and more rarely in the vertebrae (approximately 15 per cent) (Mabrey 1935, Littman 1953, Dahlin 1970. Men appear to be more exposed than women (ratio 2:l) and the most afflicted decades are the third and fourth for spheno-occipital chordomas and the fifth and sixth for sacrococcygeal chordomas.…”

“…The treatment mostly advocated in the literature is surgical ablation (e.g. Littman 1953). However, the frequently large size of the sacrococcygeal tumors and the inaccessible location of the vertebral and spheno-occipital ones make surgery difficult.…”

Live/Real Time Three‐Dimensional Transthoracic Echocardiographic Description of Chordoma Metastatic to the Heart

“…Chordomas are very rare tumors that arise from remnants of the fetal notochord 6 . They usually arise in the axial skeleton most commonly in the sacro‐coccygeal region but origin from other parts of the spine as well as the clival region has been reported 6 . They are slow growing with local invasion but multiple local recurrences have been noted after surgical resection 6,7 .…”

“…They usually arise in the axial skeleton most commonly in the sacro‐coccygeal region but origin from other parts of the spine as well as the clival region has been reported 6 . They are slow growing with local invasion but multiple local recurrences have been noted after surgical resection 6,7 . Distant metastases from chordoma have been reported in 3–48% of patients most commonly to the lung, liver and lymph nodes 6–9 .…”

“…They are slow growing with local invasion but multiple local recurrences have been noted after surgical resection 6,7 . Distant metastases from chordoma have been reported in 3–48% of patients most commonly to the lung, liver and lymph nodes 6–9 . Metastasis to the heart is rare and may involve the pericardium, right atrium, RV and left ventricle 7,10–12 .…”