Segmental Schwannomatosis of the Lower Extremity – A Case Series

Abstract

Segmental schwannomatosis involving a nerve in single limb is uncommon. Schwannomatosis is used to describe a distinct clinicopathological disease of multiple schwannomas without manifestations of neurofibromatosis, and it is termed segmental when a single extremity is involved. Surgery is indicated when there is progressive clinical deterioration or progressive increase in size of the tumors. We present a case series of segmental schwannomatosis involving the lower limb.

Painful motor nerve schwannomas

“…Von Deimling et al, 14 reported a 46 year old male who had 18 separate lesions along the medial plantar division of the posterior tibial nerve who had a history of pain in his foot for 18 months prior to the diagnosis and surgery.…”