Solitary intestinal fibromatosis associated with congenital ileal atresia

Coulon, A.; Mcheik, Jiad N.; Milin, Serge; Levard, G.; Levillain, P.; Fromont, Gaëlle

doi:10.1016/j.jpedsurg.2007.08.005

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2017

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“…A solitary lesion in the abdomen though is very rare. A literature search revealed only 20 other reported cases of a solitary infantile abdominal myofibroma (Table 1 ); however, it is the first case in which anemia is the primary presentation of the underlying disease [ 2 , 3 , 4 , 5 , 6 , 7 , 8 , 9 , 10 , 11 , 12 , 13 , 14 , 15 , 16 , 17 , 18 ]. The typical presentation of an intestinal myofibroma is associated with bowel perforation or obstruction, accompanied by obstructive symptoms such as vomiting and abdominal distention [ 18 ].…”

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confidence: 99%

A Solitary Intestinal Myofibroma: A Rare Cause of Neonatal Anemia

et al. 2017

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Solitary infantile myofibroma with visceral involvement is very rare. We present an unusual case of a solitary myofibroma with abdominal localization in a 1-day-old female neonate who presented with severe anemia and rectal bleeding. A bleeding myofibroma was found, located in the wall of the jejunum, and totally resected. In case of a solitary lesion, treatment is relatively easy and effective, with excellent prognosis after total resection. The multiple form (myofibromatosis) has a poor prognosis with low survival rates. We therefore recommend total body MRI for all patients diagnosed with myofibroma to rule out other lesions.

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