Spindle‐cell rhabdomyosarcoma of the thumb: Rare site, rare tumor in a child

Mahana, Sonam; Tomar, Reena; Agarwal, Anil; Sharma, Divya; Khurana, Nita; Gupta, Ruchika

doi:10.1002/dc.23552

Cited by 2 publications

(2 citation statements)

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“…Generally, these tumors present as rapidly growing masses in the paratesticular region in young patients, but in adults it commonly arises in the head and neck. Rarely, spindle cell rhabdomyosarcoma may arise in an extremity, and it has been described on the thumb in a young child . Histologically, it has a similar composition of whorls of spindle cells, which can be arranged in a herringbone pattern, but its immunohistochemical positivity for desmin and myogenin help to differentiate it from CIFS .…”

Section: Discussionmentioning

confidence: 99%

“…Rarely, spindle cell rhabdomyosarcoma may arise in an extremity, and it has been described on the thumb in a young child. 21 Histologically, it has a similar composition of whorls of spindle cells, which can be arranged in a herringbone pattern, but its immunohistochemical positivity for desmin and myogenin help to differentiate it from CIFS. 19,20 Our case was negative for myogenin and desmin.…”

Section: -11mentioning

confidence: 99%

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Congenital infantile fibrosarcoma mimicking a cutaneous vascular lesion: a case report and review of the literature

et al. 2016

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Congenital infantile fibrosarcoma (CIFS) is a rare neoplasm of infancy that occurs most frequently in the extremities, and when presenting in the skin, may sometimes resemble infantile hemangiomas or other vascular lesions. Clinically, these tumors differ from hemangiomas in the time of onset, morphology, and growth pattern and must be evaluated histologically for definitive diagnosis. We describe an infant with a neoplasm involving the distal left forearm initially presumed to be a vascular lesion after evaluation by two separate ultrasound studies. He presented at seven weeks of life with a multinodular lesion that had enlarged significantly since birth, and the skin biopsy revealed a fibrosarcoma. This case highlights an unusual cutaneous presentation of CIFS, which varies in appearance from the previous 12 cases reported in the literature. We review the clinical manifestations of these congenital masses and emphasize early diagnosis for conservative therapy and improved prognosis.

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Section: Discussionmentioning

confidence: 99%