Spontaneous Chylothorax in Newborns

Caso Clínico Radiológico para diagnóstico

“…El quilotórax (QT) se define como la acumulación de quilo, es decir linfa de origen intestinal en la cavidad pleural, que se escapa desde el conducto torácico (CT) o de sus ramas [1][2][3] . El QT pueden ser: a) congénito por laceraciones del CT debidas a parto traumático, incremento súbito de la presión venosa fetal durante el período expulsivo, anormalidades del CT, como atresia o hipoplasia y a diversos síndromes genéticos como Síndrome de Down, Síndrome de Noonan, Síndrome de Turner, linfangiectasia pulmonar, fístula tráqueo-esofágica del tipo H, secuestro extralobar, entre otros [1][2][3][4] .…”

Chylothorax in Infants and Children

“…14 There are reports of the successful use of radiotherapy for cases in which chylothorax was refractory to surgical management. 16,17 Chylothorax can be a manifestation of Down, [18][19][20][21] Turner, [18][19][20] and Noonan syndromes. [18][19][20][22][23][24] Congenital and pulmonary lymphangiectasia occur in these syndromes.…”

“…16,17 Chylothorax can be a manifestation of Down, [18][19][20][21] Turner, [18][19][20] and Noonan syndromes. [18][19][20][22][23][24] Congenital and pulmonary lymphangiectasia occur in these syndromes. 2 Other syndromes associated with chylothorax are X-linked myotubular myopathy, 25 35 Anecdotal reports suggest that interferon a2b may be trialed in the treatment of this disease.…”

Congenital chylothorax: current perspectives and trends

“…1 The most serious consequences of fetal chylothorax are pulmonary hypoplasia, congestive heart failure, and hydrops. 1,2,5 CC can be an isolated manifestation or may be associated with genetic conditions such as trisomy 21 (which is associated with 4.9% of isolated pleural effusions), monosomy X, 1,2 Turner, 4,6,7 and Noonan syndromes 4,6,7 (Table 1). Congenital lymphangiectasia can occur as part of these conditions.…”