Successful Pregnancy, Epidural Anaesthesia, Labour, and Delivery in a Woman With Sturge-Weber Syndrome and Previous Hemispherectomy

Aziz, Aly Shah; Hui, Dini; Chinnappa, Vinod; Aviv, Richard I.; Swartz, Richard H.

doi:10.1016/s1701-2163(15)30814-8

Cited by 8 publications

(8 citation statements)

References 7 publications

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“…8 Another woman with SWS is reported to have two vaginal deliveries and uncomplicated epidurals, but she had a hemispherectomy performed as a child with no residual leptomeningeal angiomatosis (with noncontrast imaging). 14 In summary, SWS is a rare condition. There is a recognised need for consensus guidelines on care and surveillance as these children grow into adulthood 20 as there is little understood about disease progression in the skin, eye and brain.…”

Section: Discussionmentioning

confidence: 99%

“…Klippel-Trenaunay syndrome (KTS) or Parkes Weber syndrome (PWS). Regional anaesthesia has been performed successfully in pregnancy 9,14 and is the preferred technique by many. 15 Epidural anaesthesia also has benefits for labouring parturients in avoiding increases in intracranial pressure and allowing for an assisted second stage of labour if required.…”

Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

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Sturge-Weber syndrome: Case report, literature review and proposed pregnancy care plan

2021

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The pregnancy of a 38-year-old woman with Sturge-Weber syndrome and epilepsy is described here, with safe outcome for mother and baby despite considerable controversy about peripartum care. Literature review reveals seven case reports of pregnancy in women with Sturge-Weber syndrome and there is little to guide clinicians in the management of these complex cases. A care pathway for women with Sturge-Weber syndrome that are planning pregnancy or are pregnant is proposed.

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Section: Discussionmentioning

confidence: 99%

Section: Discussionmentioning

confidence: 99%

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Sturge-Weber syndrome: Case report, literature review and proposed pregnancy care plan

2021

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“…[ 12 ] Fortunately, the patient underwent elective cesarean delivery successfully with slowly titrated epidural anesthesia. [ 13 ] Subcutaneous treprostinil administered after delivery resulted in a significant decrease in systolic PAPs, and her postoperative period was uneventful. The dosing regimens of intravenous and subcutaneous treprostinil were similar to those used for standard pulmonary hypertension treatment.…”

Section: Discussionmentioning

confidence: 99%

A case report of pulmonary arterial hypertension in pregnancy and complications of anticoagulation therapy

Xiang

Sun³

2018

Medicine

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Rationale:Treprostinil, a potent vasodilator, is the treatment of choice for severe pulmonary arterial hypertension (PAH) during pregnancy. Its inhibition of platelet aggregation increases the risk of hemorrhage. In addition, anticoagulation therapy is widely used in pregnancy with PAH due to the hypercoagulable state. However, very little is known about the complications of anticoagulants’ use in pregnancy with PAH.Patient concerns:A 27-year-old pregnant woman was admitted to the hospital at 32weeks with progressive dyspnea.Diagnoses:The pregnant was diagnosed with ventricular septal defect 12 years prior to presentation. Combining clinical manifestation with results of right heart catheterization (RHC) and echocardiography, it was consistent with severe World Health Organization (WHO) group I PAH.Interventions:Supportive treatment included supplemental oxygen, intravenous treprostinil, sildenafil and prophylactic anticoagulation.Outcomes:Gastrointestinal bleeding is occurred in our patient when dalteparin were used in conjunction with treprostinil. Her care was further complicated refractory to usual conservative measures before delivery.Lessons:This case report illustrates the complexities that arise when prostacyclin therapies are combined with necessary anticoagulation in patients with PAH during pregnancy. More intention should play to the complications of anticoagulant in pregnancy with PAH during treprostinil therapy.

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“…It is likely that having excellent clinical stability and high functional status after definitive treatment for Sturge Weber syndrome as a child significantly lowered the pregnancy-associated risks for patient. 6 There are specifications about anaesthesia given during caesarean section as well. That it should not increase the intracranial tension.…”

Section: Discussionmentioning

confidence: 99%

A rare case of pregnancy with Sturge-Weber syndrome

Pandey

Deshmukh

Jadhav

et al. 2015

Int J Reprod Contracept Obstet Gynecol

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Successful Pregnancy, Epidural Anaesthesia, Labour, and Delivery in a Woman With Sturge-Weber Syndrome and Previous Hemispherectomy

Cited by 8 publications

References 7 publications

Sturge-Weber syndrome: Case report, literature review and proposed pregnancy care plan

Sturge-Weber syndrome: Case report, literature review and proposed pregnancy care plan

A case report of pulmonary arterial hypertension in pregnancy and complications of anticoagulation therapy

A rare case of pregnancy with Sturge-Weber syndrome

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