Surgery for multiple and diffuse pulmonary arteriovenous fistulas during childhood

Abstract

We report an uncommon clinical case of multiple, diffuse pulmonary arteriovenous fistulas that occurred during childhood. A 15-year-old Japanese girl with multiple pulmonary arteriovenous fistulas presented with moderate hypoxemia and was treated by left lower lobectomy for complete resection of the arteriovenous fistulas. Clinical and radiographic features are presented.

Lobar occlusion of pulmonary arteriovenous malformations with Amplatzer vascular plug

“…For diffuse PAVM, completion of transcatheter embolization and significant improvement of the profound hypoxia are difficult to achieve. 2 Moreover, complete resection is considered if diffuse PAVM are localized in a lobe, 3 as in the present case.…”

“…Jun Noguchi, 1 Hitoshi Kanno, 3 Diamond-Blackfan anemia (DBA) is a rare blood disorder characterized by a failure of the bone marrow to produce enough red blood cells (RBC), and various congenital anomalies. 1 DBA must be differentiated from other anemias with low reticulocyte count.…”

Tratamiento quirúrgico de fístula arteriovenosa pulmonar en telangectasia hemorrágica hereditaria (Enfermedad de Rendu Osler Weber)

“…La embolización ha demostrado ser segura y obtener buenos resultados con las ventajas propias de los tratamientos percutáneos 4-6 . La cirugía resectiva continúa teniendo un rol en los casos en que la embolización falla o no es posible realizar, en cirugías de urgencia por rotura y sangrado, o en las FAVP de gran tamaño como en nuestra paciente, en que la lesión era única y comprometía extensamente el lóbulo medio 1,[12][13][14][15][16][17] .…”