Surgical Correction of Trigonocephaly: Theoretical Basis and Operative Procedures

Abstract

Trigonocephaly involves premature fusion of both the metopic suture and the sutures in the skull base. Surgical treatment by opening of the prematurely fused metopic suture and expansion of the anterior cranial base by creating “neosutures” was used to treat three children with trigonocephaly . The combi nation of lateral canthal advancement and radical forehead remodeling achieved excellent results . These procedures can also prevent the development of midface hypoplasia such as hypotelorism . The two younger patients, aged 0 and 6 months, achieved rapid bone growth in the defects and normaliza tion of intercanthal and interpupillary distances. The older patient, aged 8 years, retained some skull defects at follow-up.The optimal age for surgery is 3-6 months, which allows good cosmetic results and minimizes visual repercussions with relatively low perioperative risks.

New Severity Indices for Quantifying Single-Suture Metopic Craniosynostosis

“…To date, shape analysis of metopic synostosis has been used in clinical and research settings to predict the outcome of reconstructive procedures (2, 3, 6, 10, 11, 19, 21–23). There are many other practical applications for which our proposed severity indices would be useful.…”

Interdisciplinary Rehabilitation of a Patient With Opitz C-Syndrome and Extensive Craniofacial Malformation

“…The age where developmental delay is expected is estimated between three months and one year. 3,9,10,14 Lalatta et al 15 describe a comparison of two children with C-syndrome, one operated on at 7 months of age, resulting in normal brain growth and close to normal psychomotoric development at 3 years, in contrast to a non-operated patient, who was severely retarded at 4 years. Many children are therefore operated shortly after he first X-rays and diagnosis.…”