Surgical repair of a truncus arteriosus with unilateral absence of the right proximal pulmonary artery

Furuta, Akihisa; Nagashima, Mitsugi; Hiramatsu, Takeshi; Matsumura, Goki; Yamazaki, Kenji

doi:10.1111/jocs.12848

Cited by 7 publications

(5 citation statements)

References 9 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Symptomatic treatment consists of medications such as antibiotics, expectorants and bronchodilators, the treatment of pulmonary hypertension and any other treatments for complications. Nowadays in such cases, prophylaxis is very important for respiratory syncytial virus, pneumococcus, and influenza infections [15].…”

Section: Discussionmentioning

confidence: 99%

See 1 more Smart Citation

The rare manifestation of pulmonary artery agenesis

Radovanović¹,

Janković

Popović³

et al. 2019

Srp Arh Celok Lek

View full text Add to dashboard Cite

Introduction Unilateral absence of pulmonary artery is a rare vascular malformation. Because of this anomaly, the lungs are supplied by the system of collateral arteries. Case outline We present a case of the right pulmonary artery agenesis in a female patient. She was admitted to the hospital because of hemoptysis. A computed tomography scan revealed a congenital malformation-the right lung was smaller in size, the right principal pulmonary artery had not been developed along with aberrant tortuous blood vessels. Conclusion Symptomatic therapy was applied in the case of our patient. There was no need for any surgical treatment. However, in case of massive hemoptysis embolisation or lobectomy/ pneumonectomy will probably be applied.

show abstract

Section: Discussionmentioning

confidence: 99%

“…Treatment options include revascularization surgery, pulmonary vasodilator therapy (for pulmonary hypertension), pneumonectomy, or lobectomy, embolisation of collateral hemorrhage [11][12][13][14][15][16].…”

Section: Introductionmentioning

confidence: 99%

The rare manifestation of pulmonary artery agenesis

Radovanović¹,

Janković

Popović³

et al. 2019

Srp Arh Celok Lek

View full text Add to dashboard Cite

show abstract

“…The type A3 is seen in approximately 10% of the PTA spectrum 3 . The optimal strategy and practical techniques for treating this relatively rare entity remains controversial 4‐6 . In particular, it has been reported that repair was rather challenging in patients in whom the right or the left PA arose from the subclavian artery or the contralaterally located descending aorta 1 .…”

Section: Commentmentioning

confidence: 99%

“…3 The optimal strategy and practical techniques for treating this relatively rare entity remains controversial. [4][5][6] In particular, it has been reported that repair was rather challenging in patients in whom the right or the left PA arose from the subclavian artery or the contralaterally located descending aorta. 1 On top of such an atypical course of the left PA, the presence of a bulky PLSVC made us hesitate a primary repair in our small neonate.…”

Section: Commentmentioning

confidence: 99%

Is two‐staged repair for truncus arteriosus type A3 unpractical?

et al. 2020

View full text Add to dashboard Cite

Background A complex and rare form of persistent truncus arteriosus needs careful attention when choosing the optimal strategy for repair. Aim of the Study We herein describe our surgical strategy of a small infant having this malformation concomitantly with right aortic arch, unusual pulmonary artery branching and a left superior vena cava. Methods The patient underwent initially bilateral pulmonary arterial banding followed by the Rastelli type definitive repair. The pulmonary arteries were unified in front of the left superior vena cava, and the right ventricular outflow tract was readily reconstructed. Results The patient is doing well with an excellent hemodynamic status. Conclusions: We considered the two‐stage approach was sensible in this particular patient.

show abstract

“…Conversely, approximately 30% of patients with UAPA has no associated cardiovascular anomalies, termed isolated UAPA, which are asymptomatic. [2][3][4][5] The absence of isolated pulmonary arteries was rst described by Fraentzel in 1868 [6], followed by approximately 350 cases of UAPA reported in the world literature [7,8], but there still lacks in clinical management for UAPA in infants and children.…”

Section: Introductionmentioning

confidence: 99%

Early Single-Stage Surgical Revascularization of Pulmonary Artery in Unilateral Absence of a Pulmonary Artery

Xia

et al. 2020

Preprint

View full text Add to dashboard Cite

BackgroundThis research aims to summarize the findings of the early single-stage revascularization of remnant pulmonary artery in unilateral absent intrapericardial pulmonary artery. MethodsWe retrospectively analyzed the medical records of 10 patients with unilateral absent pulmonary artery, in which 7 were right and 3 were left, the median age and median weight at surgery was 4 months and 5.2 kg, respectively. The patients received operation from January 2009 to June 2020. ResultsTen patients, 1 case associated with atrial septal defect, 2 cases with tetralogy of Fallot, and 1 case with aortopulmonary window. The median diameter of the affected hilar pulmonary artery remnants was 3.1mm (1.6-5mm), and the Z value was -3.66±1.86 (range, -6.7 to -1.75). All the patients received single-stage revascularization: tube graft interposition in 3 patients, autologous pericardial roll in 4, direct anastomosis in one, and main pulmonary artery flap angioplasty in the rest 3. No hospital deaths occurred. The follow-up period was 1 month to 5.6 years. One case underwent percutaneous balloon dilatation due to new pulmonary artery stenosis. Nonetheless, the results were encouraging, symptoms have improved in all patients. The Z value of the latest ipsilateral pulmonary artery diameter was -2.34±1.18 (range, -4.52 to -1.35), a significantly improvement when compared to the preoperative value.ConclusionsSingle-stage pulmonary artery revascularization is effective at restoring normal antegrade flow to the affected lung, resulting in improved diameter of the PA, and patient’s symptoms. However, transcatheter intervention may diminish the new pulmonary artery stenosis temporarily, reoperation is still needed in the long-term follow-up.

show abstract

Surgical repair of a truncus arteriosus with unilateral absence of the right proximal pulmonary artery

Cited by 7 publications

References 9 publications

The rare manifestation of pulmonary artery agenesis

The rare manifestation of pulmonary artery agenesis

Is two‐staged repair for truncus arteriosus type A3 unpractical?

Early Single-Stage Surgical Revascularization of Pulmonary Artery in Unilateral Absence of a Pulmonary Artery

Contact Info

Product

Resources

About